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Show Journal of CliniGlI Neuro-ophthalmology 8(2): 143, 1988. Letter to the Editor Congenital Ocular Motor Apraxia To the Editor: We recently published an article entitled, "Congenital Ocular Motor Apraxia in Twins" in the Journal of Clinical Neuro-ophthalmology (1987;7:1047). In this report, on page 106 we stated that this was the first report of magnetic resonance imaging in patients with congenital ocular motor apraxia. Mr. A. R. Fielder, FRCS, has sent me an article that shows that our report was not the first MRI publication regarding congenital ocular motor apraxia. Perhaps a short paragraph in the Journal of Clinical Neuro-ophthalmology is indicated. Kenneth W. Wright, M.D. Opthalmology and Pediatrics Childrens Hospital of Los Angeles Los Angeles, CA 90054-0700 Editorial Comment The letter above by Dr. Wright was accompanied by a reprint of the paper by Fielder AR, Gresty MA, Dodd KL, Mellor DH, & Levene MI, Congenital ocular motor apraxia [Trans Ophthalmol Soc UK 1986;105:589-98]. In that report, nine patients with congenital ocular motor apraxia were reported. Six were male, and eight were born at term. The pregnancy was normal in seven. Optokinetic responses to a vertically moving tape were 143 © 1988 Raven Press, Ltd., New York normal in eight at all ages, but were abnormal in both horizontal directions in all of the patients at the time of initial presentation. Two presented in early infancy-before the onset of head thrustsand optokinetic testing with a flag was particularly helpful at that time. Three had agenesis of the corpus callosum and two had cerebellar anomalies. One autopsy (performed in a child who died at 1 year of age in the immediate postoperative period following closure of a ventricular septal defect) showed cerebellar cortical dysplasia-micropolygyria. Neuroimaging was performed on eight patients (computed tomographic scans in seven, and magnetic resonance imaging in one). This paper showed a very nice magnetic resonance image in Fig. 2, which revealed total absence of corpus callosum, abnormally high third ventricle roof, and immature foliation of the inferior vermis. Dr. Wright quite properly acknowledges that his report was not the first one in the literature to describe magnetic resonance imaging in congenital ocular motor apraxia. Furthermore, I also had not seen the paper of Fielder et al. before this correspondence. The blessing in the whole matter, however, is that Fielder's excellent paper has now been brought to our attention, and it really is an outstanding report on congenital ocular motor apraxia and it is recommended for your careful study. Reprint requests should be addressed to A. R. Fielder FRCS, Dept. of Ophthalmology, Clinical Sciences Building, Leicester Royal Infirmary, P.O. Box 65, Leicester, LE2 7LX, England. J. Lawton Smith, M.D. |