| Title |
Orbital Involvement in Bing-Neel Syndrome |
| Creator |
Stacy, Rebecca C; Jakobiec, Frederick A; Hochberg, Fred H; Hochberg, Ephraim P; Cestari, Dean M |
| Affiliation |
Massachusetts Eye and Ear Infirmary |
| Abstract |
Bing-Neel syndrome (BNS) is defined as intracranial involvement of Waldenstrom macroglobulinemia (WM). Few cases of orbital involvement have been reported. A 51-year-old man with a history of WM developed bilateral orbitopathy and optic neuropathy. Orbital biopsy, cerebrospinal fluid studies, and neuroimaging confirmed the diagnosis of BNS involving the orbital soft tissues, optic nerves, meninges, and cauda equina. The neuro-ophthalmic manifestations resolved after parenteral and intrathecal chemotherapy in addition to autologous stem cell transplantation. The rare neuro-ophthalmic manifestations of BNS may require a multifaceted approach to therapy. |
| Subject |
Cauda Equina; Humans; Lymph Nodes; Lymph Nodes; Magnetic Resonance Imaging; Male; Middle Older people; Optic Disk; Optic Nerve Diseases; Waldenstrom Macroglobulinemia |
| Format |
application/pdf |
| Publication Type |
Journal Article |
| Collection |
Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/ |
| Publisher |
Lippincott, Williams & Wilkins |
| Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah |
| Rights Management |
© North American Neuro-Ophthalmology Society |
| Setname |
ehsl_novel_jno |
| ID |
227090 |
| Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6f79jm2/227090 |
