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Show Journal of Clinical Neuro- ophthalmology 10( 2): 145-- 151, 1990. Literature Abstracts Superior Segmental Optic Hypoplasia: A Sign of Maternal Diabetes. Kim RY, Hoyt WF, Lessel S, Narahara MH. Arch Ophthalmol 1989; 107: 1312- 5 ( Sept). [ Reprint requests to Dr. W. F. Hoyt, NeuroOphthalmology Unit, Room 126- U, School of Medicine, University of California, San Francisco, CA 94143.] The authors review 10 patients with inferior visual field defects, usually bilateral, who had superior optic nerve hypoplasia. They identified four characteristics in 17 of 20 affected eyes- superior disc entry of the central retinal artery, superior scleral halo, superior disc pallor, and thinning of superior peripapillary nerve fiber layer. All patients were born of insulin- dependent diabetic mothers. Nice disc photographs, albeit black and white, are included in this succinct and interesting article. Lyn A. Sedwick, M. D. Guillain- Barre Syndrome Presenting as a Paralysis of Accommodation. DeRespinis PA, Shen JJ, Wagner RS. Arch Ophthalmol 1989; 107: 1282 ( Sept). [ No reprint information given.] This is a case report of a seven- year- old boy with paralysis of accommodation who went on to have other neurologic problems and after lumbar puncture and other testing, was felt to have GuillainBarre syndrome. All findings improved within several weeks. Lyn A. Sedwick, M. D. The Normal Human Optic Nerve: Axon Count and Axon Diameter Distribution. Mikelberg FS, Drance SM, Schulzer M, Yidegiligne HM, Weis MM. Ophthalmology 1989; 96: 1325- 8 ( Sept). [ Reprint requests to Dr. F. S. Mikelberg, Department . of Ophthalmology, University of British ColumbIa, 2550 Willow Street, Vancouver, Be, Canada, V5Z 3N9]. 145 © 1990 Raven Press, Ltd., New York The authors used computer image analysis to count axons in 12 normal optic nerves. They found nearly one million axons and estimated 4,909 axons are lost per year. Lyn A. Sedwick, M. D. Pseudotumor and Lymphoid Tumor: Distinct Clinicopathologic Entities. Mauriello JA Jr, Flanagan Je. Surv Ophthalmol 1989; 34: 142- 8 ( Sept- Oct). [ Reprint requests to Dr. J. Mauriello, Jr., Oculoplastics and Ophthalmic Pathology Sections, Department of Ophthalmology, UMD- New Jersey Medical School, Eye Institute of New Jersey, 15 South Ninth Street, Newark, NJ 07107.] This article presents several clinical cases of these two entities and contrasts them by history, scan findings, treatment, etc. Although good information about each disease is presented, it seems a little contrived to discuss the two in this fashion, as they are not frequently confused clinically. Lyn A. Sedwick, M. D. Essential Blepharospasm and Related Dystonias. Jordan DR, Patrinely JR, Anderson RL, Thiese SM. Surv Ophtha/ mol 1989; 34: 123- 32 ( Sept- Oct). [ Reprint requests to Dr. R. L. Anderson, Department of Ophthalmology, 50 North Medical Drive, Salt Lake City, UT 84132.] The authors discuss essential blepharospasm and related disorders with a major emphasis on treatment. Drug therapy is usually ineffective, botulism injections effective but short- lived, and myectomy recommended for long- term cure by these authors. They report good results with 300 myectomies performed over the last 10 years, with 90% improvement in visual disability. If others are getting results this good and are as enthusiastic about the procedure, it is not readily apparent from the literature. Lyn A. Sedwick, M. D. |