Selective Loss of the Electroretinogram B-wave in a Patient with Creutzfeldt-Jakob Disease

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Title Journal of Neuro-Ophthalmology, June 2000, Volume 20, Issue 2
Date 2000-06
Language eng
Format application/pdf
Type Text
Publication Type Journal Article
Collection Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/
Publisher Lippincott, Williams & Wilkins
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management © North American Neuro-Ophthalmology Society
ARK ark:/87278/s60p452w
Setname ehsl_novel_jno
ID 225039
Reference URL https://collections.lib.utah.edu/ark:/87278/s60p452w

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Title Selective Loss of the Electroretinogram B-wave in a Patient with Creutzfeldt-Jakob Disease
Creator Katz, BJ; Warner, JE; Digre, KB; Creel, DJ
Affiliation Department of Ophthalmology, University of Utah Health Sciences Center, Salt Lake City, USA.
Abstract Creutzfeldt-Jakob disease (CJD) is a neurodegenerative disease characterized by movement abnormalities and dementia that inevitably progress to death. Familial, infectious, and sporadic forms of the disease are recognized. The worldwide incidence of CJD is estimated at 1:1,000,000 per year, and it affects middle-aged men and women in roughly equal proportions. The disease is caused by a unique infectious vector, the prion, which is a mutant form of a normally occurring cell surface protein found predominantly in the central nervous system. A significant proportion of patients with CJD will have visual disturbances at some point in their illness and may therefore consult a neuro-ophthalmologist. The case of a woman in whom the diagnosis of CJD was not known until autopsy is reported. Early in the course of her disease, she sought ophthalmic consultation because of vision problems.
Subject Adult; Brain/pathology; Brain Chemistry; Creutzfeldt-Jakob Syndrome/diagnosis; Creutzfeldt-Jakob Syndrome/physiopathology; Electroretinography; Female; Humans; Magnetic Resonance Imaging; Prions/analysis; Retina/physiopathology; Retinal Diseases/diagnosis; Retinal Diseases/physiopathology; Vision Disorders/diagnosis; Vision Disorders/physiopathology
OCR Text Show
Format application/pdf
Publication Type Journal Article
Collection Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/
Publisher Lippincott, Williams & Wilkins
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management © North American Neuro-Ophthalmology Society
Setname ehsl_novel_jno
ID 225030
Reference URL https://collections.lib.utah.edu/ark:/87278/s60p452w/225030