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Show LITERATURE ABSTRACTS 283 mol 1992; 113: 443-- 6 ( Apr). [ Reprint requests to Dr. G. W. Cibis, 4620 J. C. Nichols Parkway, No. 421, Kansas City, MO 64112. J A family with internal and external ophthalmoplegia is reported. Computed tomographic scanning showed absence of superior oblique, inferior oblique, and superior rectus muscles. These patients had iris transillumination defects, and the authors reason that these findings and enolase staining pattern of tissue from these patients supports a neural crest cell origin for the abnormalities. LYI/ A. Sedwick, M. D. Lithium- Induced Orbitopathy. Dick AD, Atta H, Forrester JV. Arch OphtlzalmoI1992; 110: 452- 3 ( Apr). [ No reprint information given. J A 76- year- old woman treated with lithium carbonate for 22 years presented with conjunctival chemosis. Ultrasound showed some extraocular muscle enlargement, although computed tomography " of orbital apex and cavernous sinus was normal." Lithium was discontinued, and chemosis improved; extraocular muscle size decreased. Her thyroid- stimulating hormone level was 6.05 on lithium and decreased to 3.2 off lithium. The possible interactions between lithium, the orbit, and the thyroid gland are discussed. LYI/ A. Sedwick, M. D. Causes and Prognosis in 4,278 Cases of Paralysis of the Oculomotor, Trochlear and Abducens Cranial Nerves. Richards BW, Jones FR, Jr, Younge BR. Am J Ophthalmol 1992; 113: 489- 96 ( May). [ Reprint requests to Dr. B. R. Younge, Mayo Clinic, 200 First Street S. W., Rochester, MN 55905.] The authors report on an additional 1,278 patients with third, fourth, and/ or sixth nerve palsy from the Mayo Clinic and add to these 3,000 other cases from Mayo studied by Rucker, Rush, and Younge previously. Their results are similar to those of the previous studies: " undetermined" remains the largest single diagnosis group for all palsies except multiple oculomotor nerve palsies, which generally were diagnosable and rarely undetermined. Very few patients were found on prolonged follow- up to have moved from undetermined to another diagnosis group. Lyn A. Sedwick, M. D. Congenital Oculomotor Nerve Palsy, Cerebellar Hypoplasia, and Facial Capillary Hemangioma. White WL, Mumma JV, Tomasovic JJ. Am J Ophthallllol 1992; 113: 497- 500 ( May). [ Reprint requests to Dr. J. V. Mumma, 8038 Wurzbach Road, Suite 520, San Antonio, TX 78229.] Two unrelated cases of congenital third nerve palsy, facial capillary hemangioma, and cerebellar hypoplasia are presented. Lyn A. Sedwick, M. D. Optic Disk Cupping and Electrocardiographic Abnormalities in an American Pedigree with Leber's Hereditary Optic Neuropathy. Ortiz RG, Newman N], Manoukian SV, Diesenhouse MC, Lott MT, Wallace DC. Am J Ophtlzalmol 1992; 113: 561- 6 ( May). [ Reprint requests to Dr. N. J. Newman, Neuro- Ophthalmology Unit, Emory Eye Center, 1327 Clifton Road N. E., Atlanta, GA 30322.] Thirty- six members from four generations of a family with Leber's were studied. Electrocardiography disclosed prolonged QT interval without apparent clinical symptoms, which the authors feel may represent a systemic manifestation of the 11778 mutation of mitochondrial DNA responsible for Leber's in this family. Lyn A. Sedwick, M. D. Periorbital Urticarial Drug Reaction Associated with Intravenously Administered Methylprednisolone. John GR, Stark WJ. Am J Ophthalmol 1992; 558- 90 ( May). [ Inquiries to Dr. W. J. Stark, Maumenee 327, Wilmer Institute, 600 N. Wolfe Street, Baltimore, MD 21205.) A patient with allograft rejection of his seventh corneal transplant was given intravenous methyl- J eli" N,,,,,,- ophthalmol. Vol. 12, No. 4. 1992 |