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1 Macular Cherry Red Spots in Niemann-Pick diseaseClose up view of macular cherry red spots in Niemann-Pick disease. Same patient as R2A2a. Anatomy: Retina. Pathology: Retinal ganglion cell accumulation of lipid. Disease/Diagnosis: Niemann-Pick disease. Clinical: Severe mental retardation and blindness. Fatal.Image
2 Macular Cherry Red Spots in Niemann-Pick diseaseMacular cherry red spots in Niemann-Pick disease. Same patient as R2A2b. Anatomy: Retina. Pathology: Retinal ganglion cell accumulation of lipid. Disease/Diagnosis: Niemann-Pick disease. Clinical: Severe mental retardation and blindness. Fatal.Image
3 Macular Cherry Red Spots in Tay-Sachs diseaseMacular cherry red spots in patient with Tay-Sachs disease. Anatomy: Retina. Pathology: Retinal ganglion cell accumulation of lipid. Disease/Diagnosis: Tay-Sachs disease. Clinical: Severe mental retardation and blindness. Fatal.Image
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