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TitleCreatorDescriptionSubject
51 Paraneoplastic OpsocolonusShirley H. Wray, MD, PhD, FRCPThis patient is the index case of the Anti-Ri antibody, published in Annals of Neurology in 1988 (4). The Anti-Ri antibody is recognized to be a paraneoplastic marker in patients with breast and gynecological malignancies (10). The history of this case is particularly important because she was initi...Opsoclonus; Ocular Flutter; Oscillopsia; Saccadic Oscillations; Paraneoplastic Cerebellar Syndrome; Adenocarcinoma of the Breast; Anti-Ri Antibody; Paraneoplastic Opsoclonus; Paraneoplastic Ocular Flutter; Saccadomania
52 Paraneoplastic Ocular FlutterShirley H. Wray, MD, PhD, FRCPThe patient is a 58 year old woman with known hypertension. In 1994, two weeks prior to admission she had a dramatic change in behavior with insomnia, agitation and depression. This was accompanied by "ringing of hands and anxiety for no apparent reason". She became anorexic, lost 15 pounds in weigh...Ocular Flutter; Oscillopsia; Trunkal Ataxia; Paraneoplastic Cerebellar Syndrome; Small Cell Carcinoma of the Lung; Paraneoplastic Ocular Flutter; Flutter
53 Parasellar MeningiomaShirley H. Wray, MD, PhD, FRCPThis patient is a 58 year old woman from Peru who, in 1975, developed intermittent headaches and right retro-orbital eye pain. She was seen by several ophthalmologists in South America who were unable to make a diagnosis. In March 1977 she awoke one morning with vertical diplopia most marked on look...Ptosis; Third Nerve Palsy; Aberrant Reinnervation of the Third Nerve; Oculomotor Nerve; Parasellar Meningioma; Cavernous Sinus Syndrome; Unilateral Oculomotor Third Nerve Palsy; Unilateral Third Nerve Palsy
54 Parkinsons DiseaseShirley H. Wray, MD, PhD, FRCPSee also: http://content.lib.utah.edu/cdm/ref/collection/ehsl-shw/id/298 and http://content.lib.utah.edu/cdm/ref/collection/ehsl-shw/id/93Blepharoclonus; Convergence Insufficiency; Slow Hypometric Horizontal Saccades; Saccadic Breakdown of Smooth Pursuit; Parkinson's Disease- Dopamine deficiency; Basal Ganglia; Blepharoclonus; Convergence Insufficiency; Slow Hypometric Saccades; Saccadic Breakdown of Smooth Pursuit; Parkinson's Disea...
55 NeuroblastomaShirley H. Wray, MD, PhD, FRCPThe patient is Case 27-1995 Case Records of the Massachusetts General Hospital (New Eng. J Medicine 1995, 333:579-586). The discusser was Dr. Elizabeth Engle, Associate Professor of Neurology, Harvard Medical School. The baby girl was born after a 30 week gestation, with a birth weight of 1.25 kg. T...Downbeat Nystagmus; Paraneoplastic Opsoclonus; Neuroblastoma; Primary Position Downbeat Nystagmus; Ataxia; Paraneoplastic Downbeat Nystagmus
56 Brain MRI in Multiple SclerosisAnne G. Osborn, MDSlideshow describing condition.Abducting Nystagmus; Bilateral Internuclear Ophthalmoplegia; Botulinum Toxin Therapy; Gaze Evoked Downbeat Nystagmus; Horizontal Pendular Nystagmus; Horizontal Saccadic Dysmetria; Lid Nystagmus; Multiple Sclerosis; Normal Convergence; Oscillopsia; Pendular Horizontal Oscillations; Saccadic Dysmetri...
57 Cavernous Sinus MeningiomaShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Abducting Nystagmus; Cavernous Angioma; Convergence Normal; Facial Palsy; Facial Weakness; Fisher's One-and-a-Half Syndrome; Pendular Vertical Oscillations; Pontine Hemorrhage; Unilateral Gaze Palsy Hemorrhage; Unilateral Horizontal Gaze Palsy; Unilateral Internuclear Ophthalmoplegia; Upbeat Nystag...
58 Amyotrophic Lateral SclerosisRobert H. Brown Jr, D.Phil, MDSlideshow describing condition.Bulbar Palsy; CNS Degeneration; Convergence Insufficiency; Familial Amyotrophic Lateral Sclerosis; Lou Gehrig's Disease; Saccadic Breakdown of Horizontal Pursuit; Slow Hypometric Horizontal Saccades; Superoxide Dismutase (SOD1) Gene; Supranuclear Paralysis of Up and Downgaze Degeneration
59 Cavernous AngiomaShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Cavernous Angioma; Convergence Normal; Facial Palsy; Fisher's One-and-a-Half Syndrome; Pendular Vertical Oscillations; Pontine Hemorrhage; Unilateral Gaze Palsy Hemorrhage; Unilateral Horizontal Gaze Palsy; Unilateral Internuclear Ophthalmoplegia; Upbeat Nystagmus on Upgaze
60 Progressive Supranuclear PalsyShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Acquired Ocular Motor Apraxia; Apraxia of Eyelid Opening; CNS - Degeneration Convergence absent; Convergence Insufficiency; Global Supranuclear Vertical Gaze Palsy; Impaired Initiation of Horizontal Saccades; Lid Retraction; Positive Glabella Tap; Progressive Supranuclear Palsy - Tauopthay; Progres...
61 Supranuclear Paralysis of DowngazeShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Absent Convergence; Artery of Percheron; Midbrain Infarct; Ocular Tilt Reaction; Skew Deviation; Somnolence; Supranuclear Paralysis of Downgaze Infarct; Supranuclear Paralysis of Downgaze; Vertical Oculocephalic Reflex Normal
62 Brainstem Cavernous AngiomaShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Bilateral Horizontal Gaze Palsy Hemorrhage; Bilateral Lid Nystagmus; Cavernous Angioma; Hiccup; Horizontal Gaze Evoked Nystagmus; Lid Nystagmus; Medulla Hemorrhage; Medullary Hemorrhage; Primary Position Upbeat Nystagmus; Upbeat Nystagmus
63 Pontine InfarctionShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Abducting Nystagmus; Convergence Normal; Fisher's One-and-a-Half Syndrome; Pontine Infarct; Unilateral Horizontal Gaze Palsy Infarct; Unilateral Horizontal Gaze Palsy; Unilateral Internuclear Ophthalmoplegia; Upbeat Nystagmus on Upgaze
64 Childhood MigraineShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Alice in Wonderland Syndrome; Macropsia - Hemi-macropsia; Metamorphopsia; Migraine Visual Aura without Headache; Occipital Lobe; Visual Phenomena
65 Eyebrow SpasmDaniel J. Costello, MDSlideshow describing condition.Bipolar Affective Disorder; Epileptic Seizures; Primary Position Left Beating Nystagmus; Rhythmic Eyebrow Spasm; Torsional Nystagmus; Tuberous Sclerosis Complex (TSC-2 DNA sequence variant)
66 Charles Bonnet SyndromeShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Charles Bonnet Syndrome; Occipital Lobe; Release Hallucinations; Visual Hallucinations
67 Thalamic Stroke and Disordered SleepKenneth C. Sassower, MDSlideshow describing condition.Absent Convergence; Absent Vertical Saccades and Pursuit Movements; Artery of Percheron; Bilateral Ptosis; Convergence Retraction Nystagmus; Global Supranuclear Paralysis of Vertical Gaze; Horizontal Gaze Evoked Nystagmus; Horizontal Saccadic Dysmetria; Intact Convergence; Lateropulsion; Ocular Dysm...
68 Progressive External OphthalmoplegiaShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Bilateral Progressive External Ophthalmoplegia (PEO); Bilateral Ptosis; Cerebellar Degeneration with Ataxia; Complete External Ophthalmoplegia; External Ophthalmoplegia Affecting Upgaze; Facial Weakness; Kearns-Sayre Syndrome; Mitochondrial Myopathy; Normal Pupils; PEO plus Atypical Retinitis Pigm...
69 Familial Amyotrophic Lateral SclerosisShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Bulbar Palsy; CNS -Degeneration; Convergence Insufficiency; Familial Amyotrophic Lateral Sclerosis; Lou Gehrig's Disease; Saccadic Breakdown of Horizontal Pursuit; Slow Hypometric Horizontal Saccades; Superoxide Dismutase (SOD1) Gene; Supranuclear Paralysis of Up and Downgaze Degeneration
70 Transient Monocular BlindnessShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Ipsilateral Internal and External Carotid Occlusive Disease; Ischemic Eye Syndrome; Low Pressure Retinopathy; Ocular Stroke; Retinal Emboli; Retinal Stroke; Sunlight Provoked Transient Monocular Blindness; Transient Monocular Blindness
71 Pendular Horizontal OscillationsShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Ataxia; Bilateral Gaze Evoked Nystagmus; Gaze Evoked Horizontal Nystagmus; Horizontal Saccadic Dysmetria; Left Beating Nystagmus; Multiple Sclerosis; Obtrusive Saccades; Oscillopsia; Pendular Horizontal Oscillations; Primary Position Horizontal Nystagmus; Saccadic Dysmetria; Titubation
72 Thalamic InfarctShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Absent Convergence; Artery of Percheron; Bilateral Ptosis; Horizontal Gaze Evoked Nystagmus; Somnolence; Supranuclear Paralysis of Downgaze Infarct; Supranuclear Paralysis of Downgaze; Thalamic Infarct; Thalamus Infarct; Top of the Basilar Syndrome; Vertical Oculocephalic Reflex Normal
73 Selective Saccadic PalsyShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Bilateral Horizontal Gaze Palsy Hypoxia; Ocular Motility; Pontine Hypoxia; Selective Saccadic Palsy After Cardiac Surgery; Supranuclear Gaze Palsy
74 Visual NeglectShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Deviation of the Eyes to the Left Under Closed Eyelids; Impaired Initiation of Horizontal Saccades to the Left; Normal Pursuit Eye Movements; Parietal Lobe Infarct
75 Downbeat NystagmusShirley H. Wray, MD, PhD, FRCPSlideshow describing condition.Downbeat Nystagmus; Oscillopsia
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