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IdentifierTitleDescriptionSubject
251 H_62H62 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeRight eye. Disc looks almost normal but superior nerve fiber layer is thinned and represents a mild form of SSOH. Same patient as H_61 and H_63. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
252 H_63H63 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeVisual fields. Right eye has mild depression. Same patient as H_61 an H_62. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
253 H_64H64 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Same patient as H_65 and H_66. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
254 H_65H65 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Same patient as H_64 and H_66. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
255 H_66H66 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeVisual field. Same patient as H_65 and H_64. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
256 H_67H67 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Right eye. Same patient as H_68 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
257 H_68H68 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Left eye. Entire nerve looks hypoplastic. Same patient as H_67 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
258 H_69H69 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeVisual field. Entire visual field is constricted. Patient's mother Type 1 diabetic. Same patient as H_68 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
259 H_70H70 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Right eye. Same patient as H_71 and H_72. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
260 H_71H71 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Left eye. Same patient as H_70 and H_72. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
261 H_72H72 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeVisual field. Entire visual field is constricted. Patient's mother Type 1 diabetic. Same patient as H_70 and H_71. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
262 H_73H73 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Left eye. Same patient as H_73. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
263 H_74H74 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeBilateral SSOH. Right eye. Same patient as H_74. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
264 H_75H75 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeSSOH with hypoplasia of whole disc. Right eye. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
265 H_76H76 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeSSOH. Right eye. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
266 H_77H77 Inferior Segmental Optic Hypoplasia (ISOH)ISOH. Superior visual field defect. Inferior choroidal crescent. Anatomy: Optic disc. Pathology: Inferior segmental optic hypoplasia (ISOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Inferior Segmental Optic Hypoplasia (ISOH)
267 H_78H78 Inferior Segmental Optic Hypoplasia (ISOH)ISOH with inferior choroidal crescent. Patient had superior visual field defect. Anatomy: Optic disc. Pathology: Inferior segmental optic hypoplasia (ISOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Inferior Segmental Optic Hypoplasia (ISOH)
268 H_79H79 Inferior Segmental Optic Hypoplasia (ISOH)ISOH. Anatomy: Optic disc. Pathology: Inferior segmental optic hypoplasia (ISOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Inferior Segmental Optic Hypoplasia (ISOH)
269 H_80H80 Chiasmal Hemioptic HypoplasiaDiscs show striking nasal hypoplasia and band atrophy. DeMorsier synrome. Congenital bitemporal hemianopia with see-saw nystagmus. Note vertically oral shape of these hypoplastic nerves. The CT scan showed the median bar of the chiasm in this patient is totally hypoplastic. Anatomy: Optic disc. Path...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
270 H_81H81 Chiasmal Hemioptic HypoplasiaDe Morsier synrome with congenital bitemporal hemianopia. Right eye. Note nasal hypoplasia of the right optic disc. Same patient as H_82. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasmOptic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
271 H_82H82 Chiasmal Hemioptic HypoplasiaDe Morsier synrome with congenital bitemporal hemianopia. Left eye. Same patient as H_81. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasm.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
272 H_83H83 Chiasmal Hemioptic HypoplasiaDe Morsier synrome with congenital bitemporal hemianopia. Note nasal hypoplasia of both optic discs. Left eye above, right eye below. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasm.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia; Chiasmic Optic Nerve Hypoplasia
273 H_84H84 Chiasmal Hemioptic HypoplasiaCongenital bitemporal hemianopia with marked bi-nasal hypoplasia. Left eye. 17 year old male. Same patient as H_85. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasm.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
274 H_85H85 Chiasmal Hemioptic HypoplasiaCongenital bitemporal hemianopia with marked bi-nasal hypoplasia. Right eye. 17 year old male. Same patient as H_84. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasm.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
275 H_86H86 Chiasmal Hemioptic HypoplasiaCongenital bitemporal hemianopia with nasal hypoplasia. 24 year old man. Same patient as H_87. Anatomy: Optic disc. Pathology: Chiasmal hemioptic hypoplasia. Disease/ Diagnosis: Congenital anomaly involving chiasm.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Chiasmal Hemioptic Hypoplasia
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