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IdentifierTitleDescriptionSubject
226 H_37H37 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscTilted (dysverted) disc in patient with high myopia. Note inferior nasal crescents with accompanying segmental hypoplasia. Man with bitemporal visual field defect. Anatomy: Optic disc, retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Cli...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
227 H_38H38 Segmental Hypoplasia; Retinal; Tilted (Dysverted) DiscRight eye. Man with tilted (dysverted) disc with inferior nasal crescent and high myopia. Same patient as H_39. Anatomy: Optic disc; Retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Clinical: Man with bitemporal visual field defects.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
228 H_39H39 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscVisual field of patient in H_38 showing upper temporal field depression caused by inferior nasal hypoplasia. Anatomy: Optic disc; Retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Clinical: Man with bitemporal visual field defects.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
229 H_40H40 Segmental Hypoplasia, Retinal, Tilted (Dysverted) Disc60 year old woman with incidental bitemporal visual field depression. Extreme tilting of optic disc with inferior nasal segmental hypoplasia. Nasal retinal ectasia. Same patient as H_41. Anatomy: Optic disc; retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental opt...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
230 H_41H41 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscCT scan of patient in H_40 showing marked nasal ectasia of the eyeballs. CT scan shows obliquely inserted optic nerves and marked nasal dysplasia of the eyeballs. Anatomy: Optic disc; retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Imag...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
231 H_42H42 Segmental Hypoplasia, Retinal, Nasal HypoplasiaVisual field of patient in H_43. Flag-like temporal field defect from patient with nasal segmental disc hypoplasia. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
232 H_43H43 Segmental Hypoplasia, Retinal, Nasal HypoplasiaNasal hypoplasia barely perceptible on disc. Nasal retinal nerve fibers are completely absent from 7:00 - 12:00. Anaotmy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
233 H_44H44 Segmental Hypoplasia, Retinal, Nasal HypoplasiaBilateral nasal hypoplasia with bilateral flag-like temporal field defect. Right eye. Same patient as H_45. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
234 H_45H45 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with bilateral flag-like temporal field defect. Left eye. Same patient as H_44. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
235 H_46H46 Segmental Hypoplasia, Retinal-Nasal HypoplasiaNasal hypoplasia with suspected nasal pit about 3:00. Right eye. Man with temporal sector field defect. Same patient as H_47. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomalyOptic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
236 H_47H47 Segmental Hypoplasia, Retinal-Nasal HypoplasiaNormal left eye. Same patient as H_46. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
237 H_48H48 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with absence of nasal nerve fiber layer and corresponding flag-like temporal field defect. Right eye. Same patient as H_49. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
238 H_49H49 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with absence of nasal nerve fiber layer and corresponding flag-like temporal field defect. Left eye. Same patient as H_48. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
239 H_50H50 Segmental Hypoplasia, Retinal-Nasal HypoplasiaRight eye. Nasal hypoplasia with nasal pit. Same patient as H_51. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
240 H_51H51 Segmental Hypoplasia, Retinal-Nasal HypoplasiaVisual field showing flag-like temporal field defect in patient shown in H_50. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Cogenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
241 H_52H52 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeHigh exit point of central retinal vessels. Superior choroidal crescent. Complete loss of nerve fiber layer entering disc from above. Inferior altitudinal field defect. Type 1 diabetic mother. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital ...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
242 H_53H53 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeSuperior segmental optic hypoplasia. High exit point of central retinal vessels. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Superior segmental optic hypoplasia (SSOH).Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
243 H_54H54 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeNote superior segmental palor. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
244 H_55H55 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeNote superior choroidal crescent. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
245 H_56H56 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeHigh exit point of central retinal vessels. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). DIsease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
246 H_57H57 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeNote, in addition to SSOH, generalized hypoplasia of nerve. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
247 H_58H58 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeRight eye. Same patient as H_59 and H_60. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
248 H_59H59 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeLeft eye. Same patient as H_58 and H_60. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
249 H_60H60 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeVisual fields. Bilateral inferior altitudinal field defects. Same patient as H_59 and H_58. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
250 H_61H61 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc SyndromeLeft eye. SSOH. Same patient as H_62 and H_63. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH)
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