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1 Pseudoxanthoma Elasticum (PXE)Pseudoxanthoma elasticum (PXE) Right eye shows angiod streaks with associated hemorrhage. Patient was 25 year old man who developed a right sided carotid cavernous fistula. Anatomy: Retina. Pathology: Pseudoxanthoma elasticum (PXE). Disease/Diagnosis: PXE with angiod streaks with associated hemorrha...Image
2 Pseudoxanthoma Elasticum (PXE)Pseudoxanthoma elasticum (PXE). Right eye. Peripheral retina shows characteristic sign of PXE called Peau d'orange. Anatomy: Retina. Pathology: Pseudoxanthoma elasticum (PXE). Disease/Diagnosis: PXE with angiod streaks with associated hemorrhage associated with carotid cavernous fistula. Clinical: V...Image
3 Pseudoxanthoma Elasticum (PXE)Pseudoxanthoma elasticum (PXE). Left eye. Peripheral retina shows characteristic sign of PXE called Peau d'orange. Anatomy: Retina. Pathology: Pseudoxanthoma elasticum (PXE). Disease/Diagnosis: PXE with angiod streaks with associated hemorrhage associated with carotid cavernous fistula. Clinical: Vi...Image
4 Pseudoxanthoma Elasticum (PXE)Pseudoxanthoma elasticum (PXE) Conjunctival signs of carotid cavernous fistula of the right eye. Anatomy: Retina. Pathology: Pseudoxanthoma elasticum (PXE). Disease/Diagnosis: PXE with angiod streaks with associated hemorrhage associated with carotid cavernous fistula. Clinical: Vision blurred in ri...Image
5 Pseudoxanthoma Elasticum (PXE)Pseudoxanthoma elasticum (PXE) Lateral view of right internal carotid angiogram showing complete occlusion of the subcranial internal carotid artery with collateral formation (so called 'rete mirabile"") filling the supraclinoid carotid artery. Also shows evidence of the carotid cavernous fistula e...Image
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