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Identifier | Title | Description | Subject |
376 |
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H_52 | H52 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | High exit point of central retinal vessels. Superior choroidal crescent. Complete loss of nerve fiber layer entering disc from above. Inferior altitudinal field defect. Type 1 diabetic mother. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital ... | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
377 |
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H_53 | H53 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Superior segmental optic hypoplasia. High exit point of central retinal vessels. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Superior segmental optic hypoplasia (SSOH). | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
378 |
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H_54 | H54 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Note superior segmental palor. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
379 |
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H_55 | H55 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Note superior choroidal crescent. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
380 |
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H_56 | H56 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | High exit point of central retinal vessels. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). DIsease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
381 |
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H_57 | H57 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Note, in addition to SSOH, generalized hypoplasia of nerve. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
382 |
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H_58 | H58 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Right eye. Same patient as H_59 and H_60. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
383 |
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H_59 | H59 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Left eye. Same patient as H_58 and H_60. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
384 |
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H_60 | H60 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Visual fields. Bilateral inferior altitudinal field defects. Same patient as H_59 and H_58. Original case identifying SSOH, or "Topless disc syndrome" from Zurich. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
385 |
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H_61 | H61 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Left eye. SSOH. Same patient as H_62 and H_63. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
386 |
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H_62 | H62 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Right eye. Disc looks almost normal but superior nerve fiber layer is thinned and represents a mild form of SSOH. Same patient as H_61 and H_63. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
387 |
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H_63 | H63 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Visual fields. Right eye has mild depression. Same patient as H_61 an H_62. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
388 |
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H_64 | H64 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Same patient as H_65 and H_66. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
389 |
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H_65 | H65 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Same patient as H_64 and H_66. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
390 |
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H_66 | H66 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Visual field. Same patient as H_65 and H_64. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
391 |
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H_67 | H67 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Right eye. Same patient as H_68 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
392 |
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H_68 | H68 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Left eye. Entire nerve looks hypoplastic. Same patient as H_67 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
393 |
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H_69 | H69 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Visual field. Entire visual field is constricted. Patient's mother Type 1 diabetic. Same patient as H_68 and H_69. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
394 |
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H_70 | H70 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Right eye. Same patient as H_71 and H_72. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
395 |
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H_71 | H71 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Left eye. Same patient as H_70 and H_72. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
396 |
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H_72 | H72 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Visual field. Entire visual field is constricted. Patient's mother Type 1 diabetic. Same patient as H_70 and H_71. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
397 |
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H_73 | H73 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Left eye. Same patient as H_73. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
398 |
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H_74 | H74 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | Bilateral SSOH. Right eye. Same patient as H_74. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
399 |
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H_75 | H75 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | SSOH with hypoplasia of whole disc. Right eye. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |
400 |
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H_76 | H76 Superior Segmental Optic Hypoplasia (SSOH) Topless Disc Syndrome | SSOH. Right eye. Anatomy: Optic disc. Pathology: Superior segmental optic hypoplasia (SSOH). Disease/ Diagnosis: Congenital anomaly. | Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Superior Segmental Optic Hypoplasia (SSOH) |