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IdentifierTitleDescriptionSubject
351 H_27H27 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Right eye. Elevated hypoplastic dysplasia with anomalous vessels. Same patient as H_28. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
352 H_28H28 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Left eye. Elevated hypoplastic dysplasia with tortuous anomalous vessels. Same patient as H_27. Anatomy: Optic disc. Pathology: Dyplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
353 H_29H29 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Right eye. Dysplasia with anomalous cilioretinal arterioles. Central retinal artery may be absent. Same patient as H_30. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
354 H_30H30 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Left eye. Elevated dysplasia with anomalous cilioretinal vessels. Central retinal artery may be absent. Same patient as H_29. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
355 H_31H31 Dysplasia with Hypoplasia (Elevated Hysplasia with Anomalous Vessels)Left eye. 26 year old man. Dysplasia with hypoplasia. Father of patient in H_32. Same patient as H_10. Son of patient in H_11 an H_12. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
356 H_32H32 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Left eye. 6 year old boy. Severe dysplasia. Elevated dysplasia with medullated (myelinated) nerve fibers and anomalous vessels. Son of patient in H_31 and H_10. Grandson of patient in H_11 an H_12. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia wi...Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
357 H_33H33 Dysplasia with Hypoplasia (Elevated Dysplasia with Anomalous Vessels)Left eye. Elevated dysplasia, hypoplasia. Pseudo papilledema. Woman. Congenital optociliary bypass at 7:00. Anatomy: Optic disc. Pathology: Dysplasia of the optic disc. Disease/ Diagnosis: Elevated dysplasia with hypoplasia.Optic Disc; Congenital Anomalies; Dysplasia with Hypoplasia
358 H_34H34 Segmental Hypoplasia, Retinal-Congenital ToxoLeft eye. Temporal sector hypoplasia from congenital retinal toxoplasmosis. Note the sector shaped nerve fiber loss between 2:00 and 4:00. Same patient as H_35. Anatomy: Optic disc; retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Congenital Toxo; Toxoplasmosis
359 H_35H35 Segmental Hypoplasia, Retinal-Congenital ToxoLeft eye. Moving out temporally to see large chorioretinal scar. Temporal sector hypoplasia from congenital retinal toxoplasmosis. Same patient as H_34. Anatomy: Optic disc; Retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasiaOptic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Congenital Toxo; Toxoplasmosis
360 H_36H36 Segmental Hypoplasia, Retinal, Congenital ToxoLeft eye. Optic disc hypoplasia from congenital nasal retinal toxoplasma lesion. Chorioretinal scar. Anatomy: Optic disc, retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Congenital Toxo; Toxoplasmosis
361 H_37H37 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscTilted (dysverted) disc in patient with high myopia. Note inferior nasal crescents with accompanying segmental hypoplasia. Man with bitemporal visual field defect. Anatomy: Optic disc, retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Cli...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
362 H_38H38 Segmental Hypoplasia; Retinal; Tilted (Dysverted) DiscRight eye. Man with tilted (dysverted) disc with inferior nasal crescent and high myopia. Same patient as H_39. Anatomy: Optic disc; Retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Clinical: Man with bitemporal visual field defects.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
363 H_39H39 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscVisual field of patient in H_38 showing upper temporal field depression caused by inferior nasal hypoplasia. Anatomy: Optic disc; Retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Clinical: Man with bitemporal visual field defects.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
364 H_40H40 Segmental Hypoplasia, Retinal, Tilted (Dysverted) Disc60 year old woman with incidental bitemporal visual field depression. Extreme tilting of optic disc with inferior nasal segmental hypoplasia. Nasal retinal ectasia. Same patient as H_41. Anatomy: Optic disc; retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental opt...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
365 H_41H41 Segmental Hypoplasia, Retinal, Tilted (Dysverted) DiscCT scan of patient in H_40 showing marked nasal ectasia of the eyeballs. CT scan shows obliquely inserted optic nerves and marked nasal dysplasia of the eyeballs. Anatomy: Optic disc; retina. Pathology: Hypoplasia secondary to retinal lesion. Disease/ Diagnosis: Segmental optic disc hypoplasia. Imag...Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal; Dysverted Disc; Tilted Disc
366 H_42H42 Segmental Hypoplasia, Retinal, Nasal HypoplasiaVisual field of patient in H_43. Flag-like temporal field defect from patient with nasal segmental disc hypoplasia. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
367 H_43H43 Segmental Hypoplasia, Retinal, Nasal HypoplasiaNasal hypoplasia barely perceptible on disc. Nasal retinal nerve fibers are completely absent from 7:00 - 12:00. Anaotmy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
368 H_44H44 Segmental Hypoplasia, Retinal, Nasal HypoplasiaBilateral nasal hypoplasia with bilateral flag-like temporal field defect. Right eye. Same patient as H_45. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
369 H_45H45 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with bilateral flag-like temporal field defect. Left eye. Same patient as H_44. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
370 H_46H46 Segmental Hypoplasia, Retinal-Nasal HypoplasiaNasal hypoplasia with suspected nasal pit about 3:00. Right eye. Man with temporal sector field defect. Same patient as H_47. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomalyOptic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
371 H_47H47 Segmental Hypoplasia, Retinal-Nasal HypoplasiaNormal left eye. Same patient as H_46. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
372 H_48H48 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with absence of nasal nerve fiber layer and corresponding flag-like temporal field defect. Right eye. Same patient as H_49. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
373 H_49H49 Segmental Hypoplasia, Retinal-Nasal HypoplasiaBilateral nasal hypoplasia with absence of nasal nerve fiber layer and corresponding flag-like temporal field defect. Left eye. Same patient as H_48. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
374 H_50H50 Segmental Hypoplasia, Retinal-Nasal HypoplasiaRight eye. Nasal hypoplasia with nasal pit. Same patient as H_51. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Congential anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
375 H_51H51 Segmental Hypoplasia, Retinal-Nasal HypoplasiaVisual field showing flag-like temporal field defect in patient shown in H_50. Anatomy: Optic disc. Pathology: Nasal segmental disc hypoplasia. Disease/ Diagnosis: Cogenital anomaly.Optic Disc; Congenital Anomalies; Segmental Hypoplasia; Retinal-Nasal Hypoplasia
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