Giant fusiform aneurysm in an adolescent with PHACES syndrome treated with a high-flow external carotid artery-M3 bypass

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Publication Type Journal Article
School or College School of Medicine
Department Neurosurgery
Creator Couldwell, William T.
Other Author Kan, Peter; Liu, James K.
Title Giant fusiform aneurysm in an adolescent with PHACES syndrome treated with a high-flow external carotid artery-M3 bypass
Date 2007
Description The acronym PHACES describes a rare neurocutaneous syndrome that comprises posterior fossa malformations, facial hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, eye abnormalities, and sternal defects. Facial hemangiomas constitute the hallmark of this disorder. Giant intracranial aneurysms have not been previously reported in the literature as manifestations of PHACES syndrome and can present difficult therapeutic challenges. The authors describe a unique case of a 13-year-old adolescent boy with an incomplete phenotypic expression of PHACES syndrome who harbored diffuse cerebral angiodysplasia and a giant fusiform internal carotid artery (ICA) aneurysm extending from the distal cavernous segment to the supraclinoid segment. The aneurysm was successfully treated with a high-flow saphenous vein graft bypass from the external carotid artery to the distal middle cerebral artery followed by proximal ICA occlusion. This case represents a unique vascular manifestation of PHACES syndrome that required a complex management strategy. The authors review the literature on this rare disorder and emphasize the importance of considering the diagnosis of PHACES syndrome in child with a facial hemangioma.
Type Text
Publisher American Association of Neurological Surgeons (AANS)
Journal Title Journal of Neurosurgery
Volume 106
Issue 6
First Page 495
Last Page 500
Language eng
Bibliographic Citation Kan, P., Liu, J. K., & Couldwell, W. T. (2007). Giant fusiform aneurysm in an adolescent with PHACES syndrome treated with a high-flow external carotid artery-M3 bypass. Case report and review of the literature. Journal of Neurosurgery, 106(6 Suppl), 495-500.
Rights Management (c) American Association of Neurological Surgeons
Format Medium application/pdf
Format Extent 417,925 bytes
Identifier ir-main,12963
ARK ark:/87278/s6zc8mh6
Setname ir_uspace
Date Created 2012-06-13
Date Modified 2012-06-13
ID 706788
Reference URL https://collections.lib.utah.edu/ark:/87278/s6zc8mh6
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