| Title |
Maffucci Syndrome and Intracranial Chondrosarcomas: A Case Report Featuring Spontaneous Resolution of Sixth Nerve Palsy |
| Creator |
Monique Munro; Fiona Costello; David Burrowes; Ryan Yau |
| Affiliation |
Section of Ophthalmology (MM, FC, RY), Department of Surgery, University of Calgary, Calgary, Alberta, Canada; Departments of Clinical Neurosciences (FC) and Radiology (DB), University of Calgary, Calgary Alberta, Canada; and Mitchell Eye Centre, Southern Alberta Eye Center, Calgary, Alberta, Canada. |
| Abstract |
Maffucci syndrome is a rare disease process characterized by enchondromatosis with cutaneous hemangiomatosis. We report a 20-year-old woman with Maffucci syndrome with a 5-day history of diplopia. She was found to have a left sixth nerve palsy due to a parasellar chondrosarcoma. Three weeks later, the patient's diplopia spontaneously resolved. This unusual clinical course prompted us to review frequency of sixth nerve palsy with skull base neoplasms and the phenomenon of spontaneous resolution of diplopia. |
| Subject |
Abducens Nerve Diseases; Brain; Chondrosarcoma; Enchondromatosis; Female; Humans; Magnetic Resonance Imaging; S100 Proteins; Young Adult |
| Format |
application/pdf |
| Publication Type |
Journal Article |
| Collection |
Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/ |
| Publisher |
Lippincott, Williams & Wilkins |
| Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah |
| Rights Management |
© North American Neuro-Ophthalmology Society |
| Setname |
ehsl_novel_jno |
| ID |
227677 |
| Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6b311f8/227677 |
