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Show Journal of Clinical Neuro-ophthalmology 13(1): 73-76, 1993. Literature Abstracts Ophthalmic Manifestations of Chronic Angioedema With Necrotizing Vasculitis. Margo CE, Stinson WG, Hamed LM, Am J Ophthalmol 1992; 113:691-6 (June). [Reprint requests to Dr. C. E. Margo, Department of Ophthalmology, University of Florida, Box 100284, JHMHSC, Gainesville, FL 32610-0284. ] Two patients with angioedema of the eyelids and orbits are described in whom skin biopsy disclosed a necrotizing vasculitis. This condition is discussed with highlighting of ophthalmic manifestations. Lyn A. Sedwick, M.D. Giant Cell Arteritis in the Ocular Ischemic Syndrome. Hamed LM, Guy JR, Moster ML, Bosley T. Am JOphthalmoI1992;113:702-5 (June). [Reprint requests to Dr. L. M. Hamed, Department of Ophthalmology, College of Medicine, University of Florida, Box 100284, JHMHSC, Gainesville, FL 32610-0284, ] Four patients with ocular ischemic syndrome (hypotony, uveitis, corneal edema, and visual loss resulting from decreased ocular perfusion) were found to have biopsy-proven giant cell arteritis. Three patients had jaw claudication, one of these had headaches, and one patient had only ocular pain. Another unusual but important presentation of this disease. Lyn A. Sedwick, M.D. Joubert's Syndrome, Ocular Fibrosis, and Normal Histidine Levels. Jacobson OM, Johnson R, Frens DB. Am JOphthalmoI1992;1l3:714-6 (June). [Inquiries to Dr. D. M. Jacobson, Neuro-ophthalmology (4F), Marshfield Clinic, 1000 N. Oak Ave., Marshfield, WI 54449.] An infant with Joubert's syndrome also was found to have probable ocular fibrosis and his- 73 © 1993 Raven Press, Ltd., New York tidinemia, The authors believe these two diagnoses may be related and recommend histidine assays on patients with Joubert's or ocular fibrosis. Lyn A. Sedwick, M.D. Long-Term Results of Adjustable Suture Surgery for Strabismus Secondary to Thyroid Ophthalmopathy. Lueder GT, Scott WE, Kutschke PI, Keech RV. Ophthalmology 1992;99:993-7 (June). [Reprint requests to Dr. W. E. Scott, University of Iowa Hospitals and Clinics, Department of Ophthalmology, Iowa City, IA 52242.] Records of 1524 patients with thyroid ophthalmopathy were reviewed and 47 identified who had adjustable suture surgery with average follow-up of 41 months. Results were good or excellent in 73%, fair in 19%, and poor in 9%. Complications of the surgery are discussed as is the use of prisms. The authors feel adjustable sutures are an effective surgical therapy in selected patients with thyroid ophthalmopathy. Lyn A. Sedwick, M.D. Intraocular and Central Nervous System Lymphoma in a Cardiac Transplant Recipient. Johnson BL. Ophthalmology 1992;99:987-92 (June), [Reprint requests to Dr. B. L. Johnson, Eye Pathology Laboratory, Eye and Ear Institute, 203 Lothrop St., Pittsburgh, PA 15213. J A 69-year-old lady on cyclosporine and azathioprine following heart transplant 2 years previously developed vitreous cells and retinal infiltrates thought to be secondary to toxoplasmosis. She responded only partly to appropriate therapy for toxoplasmosis and ultimately had increased vitreous cells, decreased ocular motility, and an orbital mass with cranial extension on magnetic resonance scan, biopsy of which showed large-cell malignant lymphoma (reticulum cell sarcoma). Autopsy |