Title |
Bilateral Optic Neuropathy Associated with Diffuse Cerebral Angiomatosis in Sturge-Weber Syndrome |
Creator |
Sadda, SR; Miller, NR; Tamargo, R; Wityk, R |
Affiliation |
Wilmer Ophthalmological Institute, Department of Neurosurgery, The Johns Hopkins Medical Institutions, Baltimore, Maryland, USA. |
Abstract |
Visual loss in patients with encephalotrigeminal angiomatosis or Sturge-Weber syndrome usually results from secondary glaucoma or from damage to the retrogeniculate pathways by the angiomatous lesions. Optic neuropathy has not been reported as a component of this syndrome. This report describes a patient who developed bilateral optic neuropathy with progressive visual loss associated with diffuse cerebral angiomatosis in the setting of Sturge-Weber syndrome. |
Subject |
Adult; Angiomatosis/complications; Biopsy; Blindness/etiology; Brain Diseases/complications; Brain Diseases/pathology; Female; Frontal Lobe/pathology; Humans; Magnetic Resonance Imaging; Optic Disk/pathology; Optic Nerve Diseases/etiology; Sturge-Weber Syndrome/complications; Sturge-Weber Syndrome/pathology; Visual Acuity; Visual Fields |
Format |
application/pdf |
Publication Type |
Journal Article |
Collection |
Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/ |
Publisher |
Lippincott, Williams & Wilkins |
Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah |
Rights Management |
© North American Neuro-Ophthalmology Society |
Setname |
ehsl_novel_jno |
ID |
225050 |
Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6vx3nmn/225050 |