Uveoencephalitis in a Young Adult

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Identifier walsh_2002_s1_c4
Title Uveoencephalitis in a Young Adult
Creator Martin W. ten Hove
Subject Subacute Sclerosing Panencephalitis; Nystagmus, Pathologic; Retinal Vasculitis; Macular Degeneration; Choroid Diseases
History A 30-year old male with a 3-week history of hemiparesis and dysphasia. Previous history significant for dysarthria, upper extremity paresis and a chronic ulcerative skin condition. Bilateral posterior uveitis manifest at age 20.
Pathology Neuronal cell loss, gliosis, foamy macrophages, and Cowdy A nuclear inclusion bodies.
Disease/Diagnosis Subacute Sclerosing Panencephalitis (SSPE)
Clinical VA: Best corrected, 6/60 OD, 6/90 OS.
Presenting Symptom Hemiparesis; Dysphasia
Neuroimaging MRI
Treatment Steroids; Antineoplastic agents
Date 2002
References 1. Jabbour JT, Duenas DA, Sever JL, Krebs HM, Horta-Barbosa L. Epidemiology of subacute sclerosing panencephalitis (SSPE). A report of the SSPE registry. JAMA;220(7):959-62 1972. 2. Anlar B, Yalaz K, Oktem F, Kose G. Long-term follow-up of patients with subacute sclerosing panencephalitis treated with intraventricular a-interferon. Neurology 1997; 48:526-528. 3. Green SH, Wirtschafter JD. Ophthalmoscopic findings in subacute sclerosing panencephalitis. Brit J Ophthal 1973; 57:780. 4. Zagami AS, Lethlean AK. Chorioretinitis as a possible very early manifestation of subacute sclerosing panencephalitis. Aust NS J Med 1991; 21. 5. Nguyen NQ, Lee AGL, McClure CD, Miller G. Subretinal Lesions in Subacute Sclerosing Panencephalitis. Journal of AAPOS 1999; 3:252-254. 6. Font RL, Jenis MAJ, Tuck KD. Measles Maculopathy Associated with Subacute Sclerosing Panencephalitis. Arch Pathol 1973; 168-174. 7. Park DW, Boldt HC, Massicotee SJ, Akang EEU, Ross KL, Bodnar A, Pless J, Ghetti B, Pascuzzi M. Subacute sclerosing panencephalitis manifesting as viral retinitis: clinical and histopathologic findings. Am J Ophthal 1997; 123:533-542.
Language eng
Format application/pdf
Type Text
Source 28th Annual North American Neuro-Ophthalmology Society Meeting, Frank B. Walsh Session CD-ROM
Relation is Part of Case 4, Session I, Walsh Session, NANOS 2002
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6rr21zn
Contributor Primary ten Hove, M.W.
Contributor Secondary Rossiter, J.; Melanson, M.; Karnauchow, T.
Setname ehsl_novel_fbw
ID 177689
Reference URL https://collections.lib.utah.edu/ark:/87278/s6rr21zn
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