Identifier |
walsh_2002_s1_c4 |
Title |
Uveoencephalitis in a Young Adult |
Creator |
Martin W. ten Hove, MD |
Affiliation |
Kingston, Ontario, Canada |
Subject |
Subacute Sclerosing Panencephalitis; Nystagmus, Pathologic; Retinal Vasculitis; Macular Degeneration; Choroid Diseases |
History |
A 30-year old male with a 3-week history of hemiparesis and dysphasia. Previous history significant for dysarthria, upper extremity paresis and a chronic ulcerative skin condition. Bilateral posterior uveitis manifest at age 20. |
Pathology |
Neuronal cell loss, gliosis, foamy macrophages, and Cowdy A nuclear inclusion bodies. |
Disease/Diagnosis |
Subacute Sclerosing Panencephalitis (SSPE) |
Clinical |
VA: Best corrected, 6/60 OD, 6/90 OS. |
Presenting Symptom |
Hemiparesis; Dysphasia |
Neuroimaging |
MRI |
Treatment |
Steroids; Antineoplastic agents |
Date |
2002 |
References |
1. Jabbour JT, Duenas DA, Sever JL, Krebs HM, Horta-Barbosa L. Epidemiology of subacute sclerosing panencephalitis (SSPE). A report of the SSPE registry. JAMA;220(7):959-62 1972. 2. Anlar B, Yalaz K, Oktem F, Kose G. Long-term follow-up of patients with subacute sclerosing panencephalitis treated with intraventricular a-interferon. Neurology 1997; 48:526-528. 3. Green SH, Wirtschafter JD. Ophthalmoscopic findings in subacute sclerosing panencephalitis. Brit J Ophthal 1973; 57:780. 4. Zagami AS, Lethlean AK. Chorioretinitis as a possible very early manifestation of subacute sclerosing panencephalitis. Aust NS J Med 1991; 21. 5. Nguyen NQ, Lee AGL, McClure CD, Miller G. Subretinal Lesions in Subacute Sclerosing Panencephalitis. Journal of AAPOS 1999; 3:252-254. 6. Font RL, Jenis MAJ, Tuck KD. Measles Maculopathy Associated with Subacute Sclerosing Panencephalitis. Arch Pathol 1973; 168-174. 7. Park DW, Boldt HC, Massicotee SJ, Akang EEU, Ross KL, Bodnar A, Pless J, Ghetti B, Pascuzzi M. Subacute sclerosing panencephalitis manifesting as viral retinitis: clinical and histopathologic findings. Am J Ophthal 1997; 123:533-542. |
Language |
eng |
Format |
application/pdf |
Type |
Text |
Source |
28th Annual North American Neuro-Ophthalmology Society Meeting, Frank B. Walsh Session CD-ROM |
Relation is Part of |
Case 4, Session I, Walsh Session, NANOS 2002 |
Collection |
Neuro-Ophthalmology Virtual Education Library: Walsh Session Annual Meeting Archives: https://novel.utah.edu/Walsh/ |
Publisher |
North American Neuro-Ophthalmology Society |
Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah |
Rights Management |
Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright |
ARK |
ark:/87278/s6rr21zn |
Setname |
ehsl_novel_fbw |
ID |
177689 |
Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6rr21zn |