| Identifier |
R1B1a |
| Title |
Sturge Weber Syndrome (Encephalotrigeminal Angiomatosis) |
| Creator |
William F. Hoyt, MD |
| Contributors |
Raphael Muci Mendoza, MD |
| Affiliation |
(WFH) Professor Emeritus of Ophthalmology, Neurology and Neurosurgery, University of California, San Francisco, California; (RM) Caracas, Venezuela |
| Subject |
Phakomatoses; Sturge-Weber Syndrome; Encephalotrigeminal Angiomatosis |
| Description |
Sturge Weber Syndrome (Encephalotrigeminal angiomatosis); Color of the retina is deep red (sometimes called tomato catsup) due to a four fold thickening of the choroidal vascular bed. Optic disc is cupped due to elevated intraocular pressure. (Secondary glaucoma) Patient had a major ""port wine"" malformation on the right forehead. These patients have superficial cerebral angiomatoses with cortical calcification. Right eye. Pair with R1_B1b. Anatomy: Choroid. Pathology: Diffuse choroidal hemangioma; Glaucoma. Disease/Diagnosis: Sturge Weber Syndrome. Clinical: Port wine hemangioma of the face. |
| Language |
eng |
| Format |
image/jpeg |
| Format Creation |
Scanned at 2700 ppi on Nikon LS2000 and Nikon 8000 film scanners |
| Type |
Image |
| Source |
35mm Kodachrome slide; 52a |
| Relation is Part of |
group R1B1 |
| Collection |
Neuro-Ophthalmology Virtual Education Library: William F. Hoyt Collection: https://novel.utah.edu/Hoyt/ |
| Publisher |
North American Neuro-Ophthalmology Society |
| Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah |
| Rights Management |
Copyright 1960. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright |
| ARK |
ark:/87278/s68s7mg9 |
| Setname |
ehsl_novel_wfh |
| ID |
189894 |
| Reference URL |
https://collections.lib.utah.edu/ark:/87278/s68s7mg9 |
