Publication Type |
Manuscript |
School or College |
School of Medicine |
Department |
Neurosurgery |
Creator |
Couldwell, William T.; Harnsberger, H. Ric |
Other Author |
Coppens, Jeroen R.; Finn, Michael A.; Sharma, Pramod |
Title |
Oronasopharyngeal chordomas |
Date |
2009 |
Description |
Background: Chordomas are rare tumors derived from notochordal remnants. The authors report on a series of three cases of primary familial oronasopharyngeal chordomas treated at our institution. Methods: A retrospective chart review was completed of the three cases of primary familial oronasopharyngeal chordoma treated at the University of Utah. Findings: All three patients (100%) were neurologically intact and presented with nasal obstruction. The patients ranged in age from 5 to 65 years and were first-degree relatives. None of the patients had bony erosion of the skull base on imaging, and all of the patients' tumors connected with the skull base via a tract. All three patients were treated with a wide excision combined with drilling of the involved skull base. They all tolerated the procedure without any complications and remain tumor free with a follow up of 12 months to 4.5 years. Conclusion: Primary oronasopharyngeal chordomas are rare tumors that may present without bony erosion of the skull base. A wide excision with drilling of the involved bony structures may offer an oncologic cure. |
Type |
Text |
Publisher |
Springer |
Volume |
151 |
Issue |
8 |
First Page |
1 |
Last Page |
26 |
Subject |
Oronasopharyngeal; Chordoma; Pharynx; Notochord; Transoral; Skull base |
Subject LCSH |
Chordoma; Skull base -- Diseases -- Treatment; Skull base -- Surgery |
Language |
eng |
Bibliographic Citation |
Coppens, J. R., Harnsberger, H. R., Finn, M. A., Sharma, P., & Couldwell, W. T. (2009). Oronasopharyngeal chordomas. Acta Neurochirurgica (Wien), 151(8), 1-26, 901-7. |
Rights Management |
(c) Springer (The original publication is available at www.springerlink.com) |
Format Medium |
application/pdf |
Format Extent |
1,061,395 bytes |
Identifier |
ir-main,12672 |
ARK |
ark:/87278/s6w95tcf |
Setname |
ir_uspace |
ID |
703193 |
Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6w95tcf |