Cerebroretinal Microangiopathy (Susac Syndrome)

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Identifier R3D1
Title Cerebroretinal Microangiopathy (Susac Syndrome)
Creator William F. Hoyt, MD
Contributors John O. Susac, MD (1940-2012)
Affiliation (WFH) Professor Emeritus of Ophthalmology, Neurology and Neurosurgery, University of California, San Francisco, California; (JOS) Neurologist, Winter Haven, Florida
Subject Occlusive Vascular Disease; Cerebroretinal Microangiopathy; Susac Syndrome; Retinocochleocerebral Vasculopathy
Description Retinal signs of Susac's Syndrome in acute phase consist of areas of retinal artery infarction from branch retinal artery occlusions. These patients are usually women, many of whom are demented and have hearing loss. Refs: 1) Susac, Hardiman, Sellhorst. Neurology. 1979. 29:313-316 2) Susac ""Susac's Syndrome"", Neurology. 44:591-593, 1994 3) Petty. Medicine. 77:12-40. 1998 4) Papo. Medicine 77:3-11. Anatomy: Retina. Pathology: Microangiopathy involving brain, auditory nerve and retina. Disease/Diagnosis: Cerebroretinal microangiopathy (Susac Syndrome). Clinical: Deafness, dementia, retinal focal visual field loss. Some of these patients have only one of this triad of symptoms.
Date 2002
References 1) Susac JO, Hardman JM, Selhorst JB. Microangiopathy of the brain and retina. Neurology. 1979 Mar;29(3):313-6. PMID: 571975 2) Susac JO. Susac's syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women. Neurology. 1994 Apr;44(4):591-3. PMID: 8164809 3) Petty GW, Engel AG, Younge BR, Duffy J, Yanagihara T, Lucchinetti CF, Bartleson JD, Parisi JE, Kasperbauer JL, Rodriguez M. Retinocochleocerebral vasculopathy. Medicine (Baltimore). 1998 Jan;77(1):12-40. Review. PMID: 9465861 4) Papo T, Biousse V, Lehoang P, Fardeau C, N'Guyen N, Huong DL, Aumaitre O, Bousser MG, Godeau P, Piette JC. Susac syndrome. Medicine (Baltimore). 1998 Jan;77(1):3-11. Review. PMID: 9465860
Language eng
Format image/jpeg
Format Creation Scanned at 2700 ppi on Nikon LS2000 and Nikon 8000 film scanners
Type Image
Source 35mm Kodachrome slide; 52a
Relation is Part of group R3D1
Collection Neuro-Ophthalmology Virtual Education Library: William F. Hoyt Collection: https://novel.utah.edu/Hoyt/
Publisher North American Neuro-Ophthalmology Society
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management Copyright 1960. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6wx0f6z
Setname ehsl_novel_wfh
ID 190013
Reference URL https://collections.lib.utah.edu/ark:/87278/s6wx0f6z
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