| Description |
One in 30,000 infants develops a congenital disease of the central nervous system (CNS), Dandy-Walker Syndrome.1 This disease consists of anatomical malformations of the cerebellum, fourth ventricle, posterior fossa, and foramina which often results in hydrocephalus and upward displacement of the lateral sinuses.1-5 Such malformations commonly result in increase intracranial pressure (ICP) and anatomical distortions of the face and skull such as cleft lip/palate, high-arched palate, retrognathia (receded jaw), and poor dentition.1 Therefore, the anesthetist must prepare for a difficult airway, take measures intraoperatively to control ICP, and attentively monitor the patient post operatively.1,3-5 |
