What's In a Name? (PowerPoint)

Update item information
Identifier walsh_2011_s3_c1_ppt
Title What's In a Name? (PowerPoint)
Creator Nicholas J Volpe, MD, Northwestern University
Subject Scleritis; Diplopia; Optic Neuropathy, Ischemic; Vasculitis, Central Nervous System; Wegener Granulomatosis
Presenting Symptom Ptosis; impaired eye movements; headache; forehead numbness
History 76-year old male; five year history of muscle pain and arthralgia; four year history of PMR symptoms; gastrointestinal illness.
Clinical 20/20-2 in the right side, light perception in the left side.
Neuroimaging CT; MRI
Pathology Intraconal mass which demonstrated heterogeneous enhancement and appeared to extend to the optic canal; an extensive necrotizing process with palisading histiocytes and multinucleate giant cells with an inflammatory infiltrate, including neutrophils, lymphocytes, and plasma cells
Disease/Diagnosis Necrotizing granulomatous inflammation of the orbit and sclera without systemic disease
Treatment Low dose steroids; Mycophenolate
References 1. Woo T, Francis I, Wilcsek G, et al. Australasian Orbital and Adnexal Wegener's Granulomatosis. Ophthalmology 108(9): 1535-1542, 2001. 2. Ahmed M, Niffenegger J, Jakobiec F, et al. Diagnosis of limited ophthalmic Wegener Granulomatosis: distinctive pathologic features with ANCA test confirmation. Int Ophthalmol 28:35-46, 2008. 3. Harman L, Margo C. Wegener's Granulomatosis. Survey of Ophthalmology 42: 458-480, 1998. 4. Rao J, Weinberger M, Oddone E. The Role of Antineutrophil Cytoplasmic Antibody (c-ANCA) Testing in the Diagnosis of Wegener Granulomatosis. Annals of Internal Medicine 123:925-932, 1995
Relation is Part of Case presented at the NANOS 2011 Walsh Session, February 5
Contributor Primary Volpe, Nicholas
Contributor Secondary Wulc, Allan; Sasson, Jodi; Yanoff, Myron
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Date 2011-02-05
Type Text
Format application/pdf
Source 43rd Annual Frank Walsh Society Meeting
Rights Management Copyright 2011. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Language eng
ARK ark:/87278/s6j67kt0
Setname ehsl_novel_fbw
Date Created 2012-05-31
Date Modified 2021-05-06
ID 179053
Reference URL https://collections.lib.utah.edu/ark:/87278/s6j67kt0