Know Your Onions: A Case of Angiocentric Eosinophilic Fibrosis

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Identifier 20220213_nanos_posters_188
Title Know Your Onions: A Case of Angiocentric Eosinophilic Fibrosis
Creator Mary Labowsky; Bart Chwalisz; Marcela Marisglia; Anna Stagner
Affiliation (ML) (BC) (AS) Massachusetts Eye and Ear Infirmary, Boston, MA; (MM) Massachusetts General Hospital, Boston, MA
Subject Neuroimaging; Eyelid & Adnexal Disease; Neuro-ophthalmology & Systemic Disease (eg. MS, MG, Thyroid); Adult Strabismus; Diplopia; Orbit/Ocular Pathology
Description Angiocentric eosinophilic fibrosis (EAF) is an indolent, tumefactive variant of IgG4-related disease that rarely manifests as an orbital process. Diagnosis is based on clinical presentation with involvement of typical organs, subacute onset, and response to immunosuppressive therapy and classic histologic findings. Elevated serum IgG4 and plasmablast levels are supportive. Treatment includes steroids, surgical debulking or complete excision, and immunosuppression. IgG4-RD responds to treatment but incomplete responses and relapses are common.
Date 2022-02
Language eng
Format application/pdf
Type Text
Source 2022 North American Neuro-Ophthalmology Society Annual Meeting
Relation is Part of NANOS Annual Meeting 2022: Poster Session I: Orbital and Eyelid Disorders
Collection Neuro-Ophthalmology Virtual Education Library: NANOS Annual Meeting Collection: https://novel.utah.edu/collection/nanos-annual-meeting-collection/
Publisher North American Neuro-Ophthalmology Society
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management Copyright 2022. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6sejp98
Setname ehsl_novel_nam
ID 2063382
Reference URL https://collections.lib.utah.edu/ark:/87278/s6sejp98
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