Enlarged Arterial Reflexes as a Possible Clinical Sign of Segmental Optic Nerve Hypoplasia

Since the late 1970s several case series of congenital segmental optic nerve hypoplasia were published, representing a developmental disorder of the nasal, the superonasal or the superior portion of the optic disc. The four characteristic clinical signs are eccentric emergence of retinal vessels, adjacent parapapillary scleral halo, pallor of the affected optic disc portion, and thinning of the corresponding retinal nerve fiber layer.