MacIntosh, Peter W; Bogard, Agatha; Setabutr, Pete; Moss, Heather E
Myeloid sarcoma; Abdominal mass; Orbital tumor; Child
An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma.
An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma. There were no signs of systemic illness. A week later, her mother noticed more prominent right eye edema and a new bump behind the right ear with crusting and tearing of the right eye.
On exam, the patient averted to light and fixed and followed with either eye, pupils were equal, round and reactive to light; Right hypertropia with resistance to retropulsion; 2+ right lid edema and ptosis and trace left lid edema and ptosis; Abdominal exam revealed a right-sided mass; CT examination of the orbits revealed bilateral orbital and paranasal sinus masses with spiculations, calcifications and osseous destruction; MRI studies confirmed multiple T1 and T2 hypointense extra-axial masses of the calvarium, skull base and bones of the face, particularly involving the orbits, which enhanced with contrast and were slightly diffusion restricted; CT of the abdomen demonstrated right adrenal and rib masses
Presentation and imaging were classic for metastatic neuroblastoma.
Relation is Part of
Case presented at the NANOS 2013 Walsh Session, February 10
Bruce, Beau B
Phillips, Paul H
Spencer S. Eccles Health Sciences Library, University of Utah