Non-Functional Sinus Disease

Update item information
Identifier walsh_2011_s4_c3
Title Non-Functional Sinus Disease
Creator Shelton, Julie
Subject Histiocytosis, Langerhans-Cell; Orbital Neoplasms; Optic Nerve Diseases; Scotoma; Exotropia; Pupil Disorders
Presenting Symptom Loss of vision OU; Headache
History A 6-year old female with a 1-week history of worsening vision OU > OD and a 2-month history of worsening headaches.
Clinical VA: NLP OD, 20/100 OS; Color vision: none OD, 4/13 OS; RAPD OD; Central scotoma OS; Sinus abnormalities noted on MR
Neuroimaging CT; MRI
Pathology Mixed inflammatory infiltrate composed of eosinophils and histiocytes.
Disease/Diagnosis Langerhan's Cell Histiocytosis of the skull base, extending into both orbital apices, causing compressive optic neuropathies, right greater than left
Treatment Surgery; Antineoplastic agents
References 1. Hoover K, Rosenthal D, Mankin H, Langerhans Cell Histiocytosis, Skeletal Radiology, 36, 95-104, 2007. 2. DAmbrosio N, Soohoo S, Warshall C, Johnson A, Karimi S, Craniofacial and Intracranial Manifestations of Langerhans Cell Histiocytosis: Report of Findings in 100 Patients, American Journal of Roentgenology, 191, 589-597, 2008. 3. Binning M, Brockmeyer D, Novel Multidisciplinary Approach for Treatment of Langerhans Cell Histiocytosis of the Skull Base, Skull Base, 18, 53-58, 2008.
Relation is Part of Case presented at the NANOS 2011 Walsh Session, February 5
Contributor Primary Shelton, Julie
Contributor Secondary Warner, Judith; Hall, Brian; Zhou, Holly; Digre, Kathleen; Boyer, Richard
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Date 2011-02-05
Type Text
Format application/pdf
Source 43rd Annual Frank Walsh Society Meeting
Rights Management Copyright 2011. For further information regarding the rights to this collection, please visit:
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Collection Neuro-ophthalmology Virtual Education Library: NOVEL
Language eng
ARK ark:/87278/s6ff3w8h
Setname ehsl_novel_fbw
Date Created 2012-05-31
Date Modified 2021-05-06
ID 179046
Reference URL
Back to Search Results