Bilateral Orbital Masses with Uzun Kemikler (X-Ray)

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Identifier walsh_2000_s5_c5_xray
Title Bilateral Orbital Masses with Uzun Kemikler (X-Ray)
Creator Satana, Banu
Subject Papilledema; Pupil Disorders; Erdheim-Chester Disease
Presenting Symptom Left-sided periorbital headache; Retroorbital pain OD with redness
History A 51-year old male with progressive left-sided periorbital headhache and retroorbital eye pain with redness. Previous history significant for hypertension, diabetes mellitus, amblyopia OD and rhinoplasty.
Clinical VA: 20/80 OD; 20/25 OS; Color plates: 10/11 OU; RAPD OD; Tonometry: 11 OD, 15 OS
Neuroimaging CT; MRI
Pathology Diffuse xanthogranulomatous inflammation with lymphocytic and plasmacytic collections.
Disease/Diagnosis Erdheim-Chester Disease
Treatment Antineoplastic agents
References 1. Franzius C, Sciuk J, Bremer C, Kempkes M, Schober O. Determination of extent and activity with radionuclide imaging in Erdheim-Chester disease. Clinical Nuclear Medicine 1999; 24(4): 252-5. 2. Shields JA, Karcioglu ZA, Shields CL, Eagle RC, Wong S. Orbital and eyelid involvement with Erdheim-Chester disease. A report of two cases. Arch-Ophthalmol 1991 June;109(6):850-4. 3. Wright RA, Hermann RC, Parisi JE. Neurological manifestations of Erdheim-Chester disease. J Neurol- Neurosurg-Psychiatry 1999 Jan;66(1): 72-5. 4. Valmaggia C, Neuweiler J, Fretz C, Gottlob I. A case of Erdheim-Chester disease with orbital involvement. Arch-Ophthalmol 1997 Nov; 115(11): 1467-8. 5. Caparros Lefebvre D, Pruyo JP, Remy M, Wallaert B, Petit H. Neuroradiologic aspects of Chester- Erdheim disease. American Journal of Neuroradiology 1995 Apr; 16(4): 735-40. 6. Miller RL, Sheeler LR, Bauer TW, Bukowski RM. Erdheim-Chester disease. Case report and review of the literature. American Journal of Medicine 1986 Jun; 80(6): 1230-6. 7. Veyssier-Beot C, Cacoub P, et al. Erdheim Chester disease. Clinical and radiologic characteristics of 59 cases. Medicine (Baltimore) 1996 May; 75.
Relation is Part of Case 5, Session V, Walsh Session, NANOS 2000; walsh_2000_s5_c5
Contributor Primary Satana, Banu
Contributor Secondary Kaufman, David L.; Eggenberger, Eric; Santos, Ronel; Suntay, Analyn; Smolyar, Albert
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Type Image
Format image/jpeg
Source 26th Annual North American Neuro-Ophthalmology Society Meeting, Frank B. Walsh Session CD-ROM
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit:
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Collection Neuro-ophthalmology Virtual Education Library: NOVEL
Language eng
ARK ark:/87278/s6c53pj7
Setname ehsl_novel_fbw
Date Created 2006-10-24
Date Modified 2012-11-30
ID 177754
Reference URL
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