Radiologic Appearance of Unilateral Sphenoid Wing Hypoplasia in Neurofibromatosis Type I

MRI features of greater wing sphenoid hypoplasia in the setting of neurofibromatosis type 1. - Figure 1 : Orbital MRI with contrast showing right greater sphenoid wing hypoplasia. The lack of bone tissue leads to herniation of the right temporal lobe into the orbit, pushing forward the orbital contents, resulting in propotosis and anterior displacement of the lateral rectus. - Figure 2 : Axial and coronal MRIs without contrast showing nasal displacement of the right optic nerve which is pushed anteriorly at its origin (2B). The temporal lobe is herniating in the orbit, resulting in nasal displacement of the optic nerve (2C).