Neurofibromatosis Type 1 Vasculopathy Presenting as Impending Central Retinal Artery Occlusion

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Title Neurofibromatosis Type 1 Vasculopathy Presenting as Impending Central Retinal Artery Occlusion
Creator Obi C. Umunakwe; Wenlan Zhang; Xi Chen; Dilraj S. Grewal; Sidney M. Gospe 3rd
Affiliation Department of Ophthalmology, Duke University Medical Center, Durham, North Carolina
Abstract A 36-year-old man with neurofibromatosis type 1 (NF1) experienced 2 brief (<30 minute) episodes of painless, peripheral vision loss in his left eye followed by complete visual recovery. Initial examination revealed visual acuity of 20/20 bilaterally, no relative afferent pupillary defect (RAPD), full confrontational visual fields, bilateral iris Lisch nodules, and unremarkable posterior segments.
Subject Adult; Blindness / etiology; Fluorescein Angiography; Humans; Male; Neurofibromatosis 1 / diagnosis; Retinal Artery / pathology; Retinal Artery Occlusion / diagnosis; Tomography, Optical Coherence; Visual Acuity / physiology
Date 2019-06
Language eng
Format application/pdf
Type Text
Publication Type Journal Article
Source Journal of Neuro-Ophthalmology, June 2019, Volume 39, Issue 2
Collection Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/
Publisher Lippincott, Williams & Wilkins
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management © North American Neuro-Ophthalmology Society
ARK ark:/87278/s6pw28vz
Setname ehsl_novel_jno
ID 1595876
Reference URL https://collections.lib.utah.edu/ark:/87278/s6pw28vz
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