Optical Coherence Tomography Angiography Findings in Superior Segmental Optic Nerve Hypoplasia

Superior segmental optic nerve hypoplasia (SSOH) is a nonprogressive congenital optic nerve head anomaly that is characterized by a localized inferior visual field defect, superior retinal nerve fiber layer (RNFL) defect, and good visual acuity (1). Liu et al (2) demonstrated that decreased peripapillary vessel density in swept-source optical coherence tomography (OCT) angiography correlated well with the areas of RNFL thinning in patients with glaucoma. Chen et al (3) reported that various kinds of optic neuropathies showed a decrease in peripapillary vessel density on OCT angiography, regardless of the etiology of the optic neuropathy, and peripapillary vessel loss on OCT angiography correlated well with the areas of RNFL thinning seen on OCT. However, to our knowledge, there are no previous reports evaluating the retinal peripapillary capillary network in SSOH.