Walsh & Hoyt: Association of Morning Glory Disc Anomaly with the Transsphenoidal Form of Basal Encephalocele

The association of morning glory disc anomaly with the transsphenoidal form of basal encephalocele is well established (174,177,186-191). The finding of V- or tongue shaped infrapapillary depigmentation adjacent to a morning glory disc anomaly or other optic disc malformation (Fig. 3.9B) is highly associated with transsphenoidal encephalocele (92), although transsphenoidal encephalocele is also well-documented in the absence of this unique infraperipapillary retinal malformation (117).