Reversal of Visual Field Defect in the Posterior Cortical Atrophy Syndrome Associated with Low Pressure Hydrocephalus

Posterior cortical atrophy is a neurodegenerative syndrome that presents with cortical visual dysfunction including visual neglect, constructional dyspraxia, spatial disorientation, and elements of both Balints and Gerstmanns syndromes in the absence of demonstrable stroke or tumor. Visual field defects are common and usually identified by both confrontational techniques and more sensitive automated threshold sensitive perimetry. We treated a patient with PCA and low pressure hydrocephalus with progressive visual field loss documented by serial perimetry in whom the visual field improved following reduction of shunt valve opening pressure.