Bilateral Intracranial Optic Nerve and Chiasmal Involvement in IgG-4 Related Disease

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Identifier 20150224_nanos_posters_232
Title Bilateral Intracranial Optic Nerve and Chiasmal Involvement in IgG-4 Related Disease
Creator Raed Behbehani; Hmoud Al-Nomas; Adeeba Al-herz; Kenneth Katchi
Affiliation (RB) Al-Bahar Ophthalmology Center, Kuwait, Kuwait; (HAN) Zain ENT Hospital, Kuwait, Kuwait; (AA) Amiri Hospital / Department of Rheumatology, Kuwait, Kuwait; (KK) Al-Sabah Hospital /Department of Pathology Kuwait, Kuwait
Subject Igg4-Related Disease; Pachymeningitis; Rituximab; Optic Neuropathy; Chiasmal Syndrome
Description IgG-4 related disease (IgG4-RD) is a disease that can affect many organs and is characterised by lymphoplasmocytic infiltration of IgG4-positive cells, obliterative phlebitis and storiform fibrosis. Orbital and ocular adnexal involvement in IgG4-RD has been reported with reports of optic nerve involvement. Systemic steroids are the primary treatment used in IgG4-RD. However, the visual outcome is not frequently reported. We present a case of severe loss of vision due to biopsy-proven IgG4-RD bilateral intracranial optic nerve and chiasmal involvement with pachymeningitis.
Date 2015
Language eng
Format application/pdf
Type Text
Source 2015 North American Neuro-Ophthalmology Society Annual Meeting
Collection Neuro-Ophthalmology Virtual Education Library: NANOS Annual Meeting Collection: https://novel.utah.edu/collection/nanos-annual-meeting-collection/
Publisher North American Neuro-Ophthalmology Society
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
ARK ark:/87278/s6pp2chn
Context URL The NANOS Annual Meeting Neuro-Ophthalmology Collection: https://novel.utah.edu/collection/NAM/toc/
Setname ehsl_novel_nam
ID 184807
Reference URL https://collections.lib.utah.edu/ark:/87278/s6pp2chn
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