Pericardial-Pleural Effusion, Ocular Protrusion, Confusion

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Identifier walsh_1992_s3_c6
Title Pericardial-Pleural Effusion, Ocular Protrusion, Confusion
Creator Irma M. Lessell
Subject Erdheim-Chester Disease; Exophthalmos; Papilledema; Xanthomatosis; Optic Atrophy; Diplopia
History A 68-year old male with bilateral proptosis, dim, blurred vision and transient obscuration of vision with diplopia OS. Previous history significant for diabetes insipidus and problems with postural balance.
Pathology Xanthoma cells mixed with mononuclear inflammatory infiltrate
Disease/Diagnosis Erdheim-Chester Disease
Clinical VA: 20/25 OD, 20/800 OS; Color plates: 9 missed OD; All OS; RAPD > OS to OD; Exophthalmometry: 22 OD, 25 OS
Presenting Symptom Blurred vision OU; Unsteady gait
Neuroimaging MRI
Treatment Surgery
Date 1992-02-28
References 1. Miller, RL, Sheeler, LR, Bauer, TW, Bukowski, RN: Erdheim-Chester disease. Case report and review of literature. Amer J of Md. 80:1230-1236, 1986. 2. Shields, JA, Karcioglu, ZA, Shields, CL, Eagle, RC, Wong, S: Orbital and eyelid involvement with Erheim-Chester disease. A report of two cases. Arch of Ophthal. 109:850-854, 1991. 3. Alper, MG: Orbital manifestations of Erdheim-chester disease. Trans Amer Ophthal Soc. LXXXI: 64-85, 1983. 4. Lantz, B, Lange, TA, Heiner, J, Herring, GF. Erdheim-chester disease, a report of three cases. Jour of Bone Joint Surg. 71a:456-464, 1989. 5. Rozenberg, I, Wehsler, J, Koenig, S, Brun, B, Larde, D, Raulo, Y, Hazard, J, Pinudeau, Y, Coscas, G. Erdheim-Chester disease presenting as malignant exophthalmos. Brit J of Rad. 59:173-177, 1986. 6. Fink, MG, Levinson, DJ, Brown, NL, Sreekanth, S, Sobel, GW. Erdheim-Chester disease. Case report with autopsty findings. Arch Path and Lab Med. 115:619-623, 1991.
Language eng
Format application/pdf
Type Text
Source 1992 Walsh Proceedings
Relation is Part of Case presented at the NANOS 1992 Walsh Session, February 27-29
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6rx9fsr
Contributor Primary Lessell, Irma M.
Setname ehsl_novel_fbw
ID 177836
Reference URL https://collections.lib.utah.edu/ark:/87278/s6rx9fsr
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