Therapy-resistant papilledema in achondroplasia.

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Title Therapy-resistant papilledema in achondroplasia.
Creator Klara Landau, MD, FEBO; B. P. Gloor, MD
Affiliation Department of Ophthalmology, University Hospital Zurich, Switzerland.
Abstract A 20-year-old achondroplastic dwarf developed severe papilledema over a short period of time. Since the age of 3 he had a ventriculoperitoneal shunt for presumed hydrocephalus. Severe ventriculomegaly was never documented, neither in the past, nor at presentation. Intracranial pressure was high, and the shunt was obliterated. Despite prompt shunt revision and subsequent bilateral optic nerve sheath decompression the patient developed postpapilledema optic atrophy with bilateral blindness. The pathophysiology of increased intracranial pressure in achondroplasia is discussed.
Subject Achondroplasia; Adult; Blindness; Humans; Male; Optic Atrophy; Papilledema; Pseudotumor Cerebri; Ventrculoperitoneal Shunt
Date 1994-03
Language eng
Format application/pdf
Type Text
Publication Type Journal Article
Collection Neuro-Ophthalmology Virtual Education Library: Journal of Neuro-Ophthalmology Archives: https://novel.utah.edu/jno/
Publisher Lippincott, Williams & Wilkins
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah
Rights Management © North American Neuro-Ophthalmology Society
ARK ark:/87278/s6vq67q3
Setname ehsl_novel_jno
ID 224460
Reference URL https://collections.lib.utah.edu/ark:/87278/s6vq67q3
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