| Identifier |
yt1s_com_Susac_Syndrome_360p |
| Title |
Susac Syndrome |
| Creator |
Andrew G. Lee, MD |
| Affiliation |
(AGL) Chairman, Department of Ophthalmology, The Methodist Hospital, Houston, Texas; Professor of Ophthalmology, Weill Cornell Medicine, New York City, New York |
| Subject |
Branch Retinal Artery; Occlusion; BRAO; Autoimmune; Microangiopathy |
| Description |
Dr. Lee lectures medical students on Susac Syndrome. |
| Transcript |
"Alright I'm going to talk a little bit about Susac Syndrome, and that is a microangiopathy. It has predilection for the brain and the cochlea and the retina, and so it is a microangiopathy of the brain, cochlea and retina, also known as the Susac syndrome. It presents with hearing loss (lower frequency hearing loss), so they need to have an audiogram. It's usually bilateral and moderate to severe. The retina finding is branch retinal artery occlusion, and it's typically young females as you would expect with presumed autoimmune disorders, and in the brain, we're going to have multiple neurologic presentations, depending on where the lesions are. The characteristic lesion is a corpus callosal T1 hole in the corpus callosum on the MRIs. So, Susac Syndrome: young female, recurrent multifocal branch retinal artery occlusion, hearing loss bilateral symmetric severe low frequency, and brain lesions, super tentorial white matter lesions, and the T1 corpus callosal wholes. This is a diagnosis of exclusion. Fluorescein angiogram sometime shows a gas plaque which is focal area of hyperflorescence just around the vessel adjacent to the branch retinal artery occlusion. The treatment, as you would expect immunosuppressive agents: steroids, CellCept, mycophenalate the usual things. There's no cure. It is a clinical diagnosis. There's no laboratory finding, and if you don't have the corpus callosal black holes you really have to make this on a clinical basis. There's no actual test for this. So, you should think about Susac Syndrome in young females with recurrent BRAO, hearing loss, and white matter lesions." |
| Date |
2022-03 |
| Language |
eng |
| Format |
video/mp4 |
| Type |
Image/MovingImage |
| Collection |
Neuro-Ophthalmology Virtual Education Library: Andrew G. Lee Collection: https://novel.utah.edu/Lee/ |
| Publisher |
North American Neuro-Ophthalmology Society |
| Holding Institution |
Spencer S. Eccles Health Sciences Library, University of Utah, 10 N 1900 E SLC, UT 84112-5890 |
| Rights Management |
Copyright 2019. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright |
| ARK |
ark:/87278/s6e4n4pv |
| Setname |
ehsl_novel_lee |
| ID |
1751105 |
| Reference URL |
https://collections.lib.utah.edu/ark:/87278/s6e4n4pv |
