Oronasopharyngeal chordomas

Update item information
Publication Type Manuscript
School or College School of Medicine
Department Neurosurgery
Creator Couldwell, William T.; Harnsberger, H. Ric
Other Author Coppens, Jeroen R.; Finn, Michael A.; Sharma, Pramod
Title Oronasopharyngeal chordomas
Date 2009
Description Background: Chordomas are rare tumors derived from notochordal remnants. The authors report on a series of three cases of primary familial oronasopharyngeal chordomas treated at our institution. Methods: A retrospective chart review was completed of the three cases of primary familial oronasopharyngeal chordoma treated at the University of Utah. Findings: All three patients (100%) were neurologically intact and presented with nasal obstruction. The patients ranged in age from 5 to 65 years and were first-degree relatives. None of the patients had bony erosion of the skull base on imaging, and all of the patients' tumors connected with the skull base via a tract. All three patients were treated with a wide excision combined with drilling of the involved skull base. They all tolerated the procedure without any complications and remain tumor free with a follow up of 12 months to 4.5 years. Conclusion: Primary oronasopharyngeal chordomas are rare tumors that may present without bony erosion of the skull base. A wide excision with drilling of the involved bony structures may offer an oncologic cure.
Type Text
Publisher Springer
Volume 151
Issue 8
First Page 1
Last Page 26
Subject Oronasopharyngeal; Chordoma; Pharynx; Notochord; Transoral; Skull base
Subject LCSH Chordoma; Skull base -- Diseases -- Treatment; Skull base -- Surgery
Language eng
Bibliographic Citation Coppens, J. R., Harnsberger, H. R., Finn, M. A., Sharma, P., & Couldwell, W. T. (2009). Oronasopharyngeal chordomas. Acta Neurochirurgica (Wien), 151(8), 1-26, 901-7.
Rights Management (c) Springer (The original publication is available at www.springerlink.com)
Format Medium application/pdf
Format Extent 1,061,395 bytes
Identifier ir-main,12672
ARK ark:/87278/s6w95tcf
Setname ir_uspace
Date Created 2012-06-13
Date Modified 2013-02-26
ID 703193
Reference URL https://collections.lib.utah.edu/ark:/87278/s6w95tcf
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