Untreated Bilateral Optic Nerve Sheath Meningiomas Observed for 27 Years

Update Item Information
Title Untreated Bilateral Optic Nerve Sheath Meningiomas Observed for 27 Years
Creator Nikisha A. Kothari, BS, Kaushal M. Kulkarni, MD, Byron L. Lam, MD
Affiliation Department of Ophthalmology, Bascom Palmer Eye Institute, University of Miami School of Medicine, Miami, Florida
Abstract We describe a vision sparing surgical approach for optic nerve glioma. A 7-year-old girl experienced declining academic performance and social withdrawal attributed to progressive disfiguring proptosis. Three years earlier, she had undergone a limited biopsy, a course of chemotherapy, and orbital radiation therapy for a right optic nerve glioma with perineural arachnoidal gliomatosis (PAG). Because of marked proptosis, another surgery was performed via a lateral orbitotomy. After cutting a window in the thickened dura of the optic nerve, rouge colored spongy tissue was suctioned from the subarachnoid space. Small, more solidified areas were excised with unipolar cautery. Care was taken to avoid identifiable blood vessels and the optic nerve, and approximately 60%-70% of the tumor was removed. The dural window was approximated with interrupted sutures. Post-operatively, there was 9 mm reduction in right proptosis and visual acuity improved to from 20/70 to 20/60. This case illustrates the possibility of debulki optic nerve gliomas without sacrificing vision. It should be stressed that this technique is only applicable to gliomas with PAG and the durability of the surgical benefit is unknown.
Subject Older people; Disease Progression; Female; Humans; Meningioma; Middle Older people; Optic Nerve Neoplasms; Treatment Refusal; Vision Disorders; Visual Acuity
OCR Text Show
Date 2013-03
Language eng
Format application/pdf
Type Text
Publication Type Journal Article
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Lippincott, Williams & Wilkins
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah, 10 N 1900 E SLC, UT 84112-5890
Rights Management © North American Neuro-Ophthalmology Society
ARK ark:/87278/s6mp88dq
Setname ehsl_novel_jno
ID 227377
Reference URL https://collections.lib.utah.edu/ark:/87278/s6mp88dq
Back to Search Results