A Wolf in Bear's Clothing

Update item information
Identifier walsh_2013_s1_c4-1
Title A Wolf in Bear's Clothing
Creator MacIntosh, Peter W; Bogard, Agatha; Setabutr, Pete; Moss, Heather E
Subject Myeloid sarcoma; Abdominal mass; Orbital tumor; Child
Presenting Symptom An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma.
History An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma. There were no signs of systemic illness. A week later, her mother noticed more prominent right eye edema and a new bump behind the right ear with crusting and tearing of the right eye.
Clinical On exam, the patient averted to light and fixed and followed with either eye, pupils were equal, round and reactive to light; Right hypertropia with resistance to retropulsion; 2+ right lid edema and ptosis and trace left lid edema and ptosis; Abdominal exam revealed a right-sided mass; CT examination of the orbits revealed bilateral orbital and paranasal sinus masses with spiculations, calcifications and osseous destruction; MRI studies confirmed multiple T1 and T2 hypointense extra-axial masses of the calvarium, skull base and bones of the face, particularly involving the orbits, which enhanced with contrast and were slightly diffusion restricted; CT of the abdomen demonstrated right adrenal and rib masses
Neuroimaging MRI
Pathology Presentation and imaging were classic for metastatic neuroblastoma.
Disease/Diagnosis Myeloid Sarcoma
References Attached
Relation is Part of Case presented at the NANOS 2013 Walsh Session, February 10
Contributor Primary Bruce, Beau B
Contributor Secondary Phillips, Paul H
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Date 2013-02-10
Type Text
Format application/pdf
Source 45th Annual Frank Walsh Society Meeting
Holding Institution North American Neuro-Ophthalmology Association (NANOS), Copyright 2013. For further information regarding the rights to this collection, please visit http://library.med.utah.edu/NOVEL
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Language eng
ARK ark:/87278/s6qk0dwh
Setname ehsl_novel_fbw
Date Created 2013-12-12
Date Modified 2021-05-06
ID 179161
Reference URL https://collections.lib.utah.edu/ark:/87278/s6qk0dwh