A Wolf in Bear's Clothing

Update Item Information
Identifier walsh_2013_s1_c4
Title A Wolf in Bear's Clothing
Creator Peter W. MacIntosh, Agatha Bogard, Pete Setabutr, Heather E. Moss
Subject Myeloid sarcoma; Abdominal mass; Orbital tumor; Child
History An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma. There were no signs of systemic illness. A week later, her mother noticed more prominent right eye edema and a new bump behind the right ear with crusting and tearing of the right eye.
Pathology Presentation and imaging were classic for metastatic neuroblastoma.
Disease/Diagnosis Myeloid Sarcoma
Clinical On exam, the patient averted to light and fixed and followed with either eye, pupils were equal, round and reactive to light; Right hypertropia with resistance to retropulsion; 2+ right lid edema and ptosis and trace left lid edema and ptosis; Abdominal exam revealed a right-sided mass; CT examination of the orbits revealed bilateral orbital and paranasal sinus masses with spiculations, calcifications and osseous destruction; MRI studies confirmed multiple T1 and T2 hypointense extra-axial masses of the calvarium, skull base and bones of the face, particularly involving the orbits, which enhanced with contrast and were slightly diffusion restricted; CT of the abdomen demonstrated right adrenal and rib masses
Presenting Symptom An eleven-month-old African-American girl with medical history of reactive airway disease developed a bump and bags under both eyes which her mother attributed to minor trauma.
Neuroimaging MRI
Date 2013-02-10
References Attached
Language eng
Format application/pdf
Type Text
Source 45th Annual Frank Walsh Society Meeting
Relation is Part of Case presented at the NANOS 2013 Walsh Session, February 10
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Holding Institution North American Neuro-Ophthalmology Association (NANOS), Copyright 2013. For further information regarding the rights to this collection, please visit http://library.med.utah.edu/NOVEL
ARK ark:/87278/s6w986sh
Contributor Primary Bruce, Beau B
Contributor Secondary Phillips, Paul H
Setname ehsl_novel_fbw
ID 179152
Reference URL https://collections.lib.utah.edu/ark:/87278/s6w986sh
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