Another Cancerous Sinus Syndrome: Not All in the Head

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Identifier walsh_2003_s3_c4
Title Another Cancerous Sinus Syndrome: Not All in the Head
Creator Steven A. Newman, MD, University of Virginia School of Medicine
Subject Scotoma; Enchondromatosis; Hemangioma; Hemianopsia; Pupil Disorders; Oculomotor Nerve Diseases; Abducens Nerve Diseases; Optic Atrophy; Postoperative Complications
History A 21-year old female with an 8-month history of transient, unusual odor and taste. Previous history significant for amblyopia treated with glasses at age 5.
Pathology Atypical hyaline cartilage with well-differentiated chondroid tissue
Disease/Diagnosis Enchondroma of the skull base involving the left cavernous sinus and parasellar region associated with Ollier disease
Clinical VA: 20/20 OU declining to 20/70 OU; RAPD OS
Presenting Symptom Transient episodes of strong taste associated with odor.
Neuroimaging N/A
Treatment Surgery
Date 2003
References 1. Ahmed SK, Lee WC, Irving RM, Walsh AR. Is Ollier's disease an understaging of Maffucci's syndrome? Journal of Laryngology & Otology. 113(9):861-4, Sep 1999. 2. Balcer LJ, Galetta SL, Cornblath WT, Liu GT. Neuro-ophthalmologic manifestations of Maffucci's syndrome and Ollier's disease. Journal of Neuro-Ophthalmology. 19(1):62-6, 1999. 3. Bovee JV, van Roggen JF, Cleton-Jansen AM, Taminiau AH, van der Woude HJ, Hogendoorn PC. Malignant progression in multiple endochondromatosis (Ollier's disease): an autopsy-based molecular genetic study. Human Pathology. 31(10):1299-303, 2000. 4. Brazier DJ, Roberts-Harry J, Crockard A. Intracavernous chondrosarcoma associated with Ollier's disease. British Journal of Ophthalmology. 77(9):599-600, 1993. 5. Clifton AG, Kendall BE, Crockard HA, Hughes T. Intracranial chondrosarcoma in a patient with Ollier's disease. British Journal of Radiology. 64(763):633-6, 1991. 6. Ghogawala Z, Moore M, Strand R, Kupsky WJ, Scott RM. Clival chondroma in a child with Ollier's disease. Case report. Pediatric Neurosurgery. 17(1):53-6, 1991-92. 7. Hasbini A, Lartigau E, Le Pechoux C, Acharki A, Vanel D, Genin J, Le Cesne A. Chondrosarcoma in Ollier's disease. Apropos of 2 cases and review of the literature. Cancer Radiotherapie. 2(4):387-91, 1998. 8. Hofman S, Heeg M, Klein JP, Krikke AP. Simultaneous occurrence of a supra- and an infratentorial glioma in a patient with Ollier's disease: more evidence for non-mesodermal tumor predisposition in multiple enchondromatosis. Skeletal Radiology. 27(12):688-91, 1998. 9. Hopyan S, Gokgoz N, Poon R, Gensure RC, Yu C, Cole WG, Bell RS, Juppner H, Andrulis IL, Wunder JS, Alman BA. A mutant PTH/PTHrP type I receptor in enchondromatosis. Nature Genetics. 30(3):306-10, 2002. 10. Jesus-Garcia R, Bo Giovanni JC, Korukian M, Boatto H, Seixas MT, Laredo J. Use of the Ilizarov external fixator in the treatment of patients with Ollier's disease. Clinical Orthopaedics & Related Research. (382):82-6, 2001. 11. McDermott AL, Dutt SN, Chavda SV, Morgan DW. Maffucci's syndrome: clinical and radiological features of a rare condition. Journal of Laryngology & Otology. 115(10): 845-7, 2001. 12. Nakase H, Nagata K, Yonezawa T, Morimoto T, Sakaki T. Extensive parasellar chondroma with Ollier's disease. Acta Neurochirurgica. 140(1):100-1, 1998. 13. Pospiech J, Mehdorn HM, Reinhardt V, Grote W. Sellar chondroma in a case of Ollier's disease. Neurochirurgia. 32(1):30-5, Jan 1989. Ramina R, Coelho Neto M, Meneses MS, Pedrozo AA. Maffucci's syndrome associated with a cranial base chondrosarcoma: case report and literature review. Neurosurgery. 41(1):269-72, 1997. 14. Rawlings CE 3rd, Bullard DE, Burger PC, Friedman AH. A case of Ollier's disease associated with two intracranial gliomas. Neurosurgery. 21(3): 400-3,1987. 15. Schmidinger A, Rosahl SK, Vorkapic P, Samii M. Natural history of chondroid skull base lesions - case report and review. Neuroradiology, 44(3):268-71, March 2002. 16. Tibbs RE Jr, Bowles AP Jr. Maffucci's syndrome associated with a cranial base chondrosarcoma: case report and literature review. Neurosurgery. 43(2):397, 1998. 17. Traflet RF, Babaria AR, Barolat G, Doan HT, Gonzalez C, Mishkin MM. Intracranial chondroma in a patient with Ollier's disease. Case report. Journal of Neurosurgery. 70(2):274-6, 1989.
Language eng
Format application/pdf
Type Text
Source 29th Annual North American Neuro-Ophthalmology Society Meeting, Frank B. Walsh Session CD-ROM
Relation is Part of Case 4, Session III, Walsh Session, NANOS 2003
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6tq6478
Contributor Primary Newman, Steven A.
Setname ehsl_novel_fbw
ID 177673
Reference URL https://collections.lib.utah.edu/ark:/87278/s6tq6478
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