Dystonia with Eye Movement Abnormalities

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Identifier NOVEL_Cogan_26-2
Title Dystonia with Eye Movement Abnormalities
Creator David G. Cogan, MD (1908-1993)
Affiliation (DGC) Former Director of Ophthalmology, National Eye Institute, National Institutes of Health, U.S. Department of Health and Human Services
Subject Eye Movement Systems Pathology; Eye Movement Recordings
Description Clinical Signs: definite instability of the adducting eye. Clinical: EXAM: V-20/20. Lag of adduction suggesting subclin. INO but no nyst of abduct eye and no vert nyst. Lid retraction on dn gz but closes eyes when asllep (with flickering of lids when done voluntarily) Little or no vert saccades but some vert pursuit. Excell.VIDEO. No Kayser. Fleider ring. Impression: Atyp.subclin INO(due to hypertonus of lat.recti ie failure of relaxion? Also failure of lids to relax. Review of Record:2 yr Hx, tightness of voice, 1 yr Hx, (handwritten word) (handwritten word) rt arm (handwritten word). (More Hand Written Notes And Can Not Read) Review of tape: Conspicuous features were the lid retraction (despite spasticity of facial muscles), infrequency of blinking, and vertical gaze palsy; INO also present. Pt. then had a left thalamotomy with marked improvement in lid functions (no longer lid retraction & presence of blinking) but vert, gz and INO unaffected.. Male patient; facial changes were noted first, followed by retraction of the eyelids, stiffness and occasional spontaneous movement of the arms, especially on the right. Pt. of Dr. Norman Foster. 24 yr old man with prog. dystonia of 2 yrs dur.involv. side. Initial Sx was retraction of lids and diplopia. Has to support limb by sitting on hands. Has extreme facial contraction and sardonic grin. [same patient as 26-1]. Disease/ Diagnosis: Dystonia.
Date 1975; 1985
Language eng
Format video/mp4
Type Image/MovingImage
Source 3/4" Umatic master videotape
Collection Neuro-Ophthalmology Virtual Education Library: David G. Cogan Collection https://novel.utah.edu/Cogan/
Publisher North American Neuro-Ophthalmology Society
Holding Institution Spencer S. Eccles Health Sciences Library, University of Utah, 10 N 1900 E SLC, UT 84112-5890
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s6154jq3
Setname ehsl_novel_dgc
ID 177254
Reference URL https://collections.lib.utah.edu/ark:/87278/s6154jq3
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